cardiac evaluation of the infantcardiac presentation • three typical presentations depending on...
TRANSCRIPT
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Cardiac Evaluation of the Infant
CHET Education
Dec. 5, 2008
LDF
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Congenital Heart Disease
• Most common of all congenital birth defect
• Affects 8 per 1000 live births
• Prompt recognition, stabilization and referral are crucial to outcome
• Due to the complexity of this patient population these kids are most challenging even to the seasoned practitioner
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Pulmonary vs. Cardiac
• Pulmonary– No murmur
– + O2 challenge (inc Sat > 10% with 100%)
– Changes in PCO2 (inc or dec)
– CXR – small heart, parenchymal changes, atelectasis, hyperinflation, etc
– Quiet precordium
– Increased respiratory distress, tachypnea, retractions, obvious inc in WOB
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Cardiac vs. Pulmonary
• Cardiac– +/‐murmur
– ‐ O2 challenge (< 10% change in Sat in 100%)
– Quiet tachypnea
– Minimal changes in PCO2
– CXR ‐ +/‐ large heart/ pulmonary edema
– Palpation of active precordium
– More cyanosis with agitation (shunt)
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Cardiac Presentation
• Three typical presentations depending on lesion– Cyanosis
– Cardiovascular collapse
– Congestive heart failure/pulmonary overcirculation
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Cyanotic Lesions
• “5 Ts”
• Transposition
• Tetrology of Fallot with pulm atresia/ stenosis
• Tricuspid atresia
• Truncus arteriosus
• Total anomalous pulmonary venous return (obstructed)
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TGA
• Most common cyanotic lesion in newborn period 5% of all CHD
• 90% present in first day of life• Ao arises from RV; PA from LV; parallel circ• Must have mixing at Atr/Vent or ductal level• CXR oval hrt due to anterior Ao and large RV• PGE1 life saving to maintain pulm blood flow• Definitive repair – Switch and septal defect closure
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TGA
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TET
• 6‐ 10% of congenital heart disease, most common
• Constellation of large VSD, RVOT obst, overriding Ao, RVH
• Degree of cyanosis dependent on RVOT obst
• The more severe the obstruction the earlier the presentation
• Mild obstruction presents later/ “pink” TET
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TET
• CXR – boot shape 2nd to RVH
• Severe TET with pulm atresia requires PGE1 to maintain pulm blood flow (acutely)
• Definitive repair now done as a single stage primary repair (vs. BT shunt then repair )
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TET
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Tricuspid Atresia
• 1% of all CHD, 3rd most common
• No direct connection of RA to RV
• Must have ASD and shunts R > L
• RV is underdeveloped
• Ductal dependent/ PGE1 to maintain pulm blood flow
• Definitive repair BDG ‐> Fontan
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TA
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Truncus Arteriosis
• Less than 1% of all CHD• Single great artery supplies systemic, pulmonary and coronary circulation
• Degree of cyanosis depends on amount of pulmonary blood flow
• **Classically grouped with cyanotic lesions, also pulm overcirculation with some degree of CHF
• Can present with tachypnea, cardiomegaly, + murmur, bounding pulses 2nd to pulmonary run off
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Truncus
• OR cyanotic from R ‐> L shunt 2nd to respiratory disease/infection (parallel circulation)
• Early surgical intervention with RV to PA conduit
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Truncus
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Total Anomalous Pulmonary Venous Return
• Pulmonary veins drain into systemic venous circulation
• Supracardiac, cardiac, infracardiac (SVC, RA, or portal circulation)
• Systemic circulation maintained by R ‐> L shunt at atrial level (ASD)
• Obstruction most often with infradiaphragmatic connection
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TAPVR
• Significant obstruction presents with cyanosis and pulm edema
• Partial or unobstructed will present later, generally within the first 2 months with hx of poor feeding, tachypnea, wheezing and mild cyanosis
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TAPVR ‐ infracardiac
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Cardiovascular Collapse
• First 2 weeks of life
• Medical emergency
• Infants are discharged prior to the ductus closing
• Present in shock
• PGE1 life saving
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CV Collapse ‐ Lesions
• Hypoplastic left heart syndrome
• Critical aortic stenosis
• Coarctation of the Ao and interrupted aortic arch
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HLHS
• Most common cause of death during first week of life
• Diminutive LV, critical AS, mitral stenosis, hypoplastic proximal aorta
• Ductus closes, PVR reduced• Shock ensues rapidly to decrease systemic flow• PGE1,manuevers to inc PVR (parallel circ)• Three definitive options: transplant, Norwood, nothing
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HLHS
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Critical AS
• Shock 2nd to compromised systemic flow
• Ductus closes
• PGE1 again is life saving
• Airway support, inotropes, treat acidosis
• If LV too small may need Norwood
• If LV adequate, valvotomy or balloon valvuloplasty in cath lab
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Coarc/IAA
• Coarc 5‐8% of CHD, IAA < 1%
• Ductus closes, severe shock
• Discrepancy of upper and lower pulses and BP
• PGE1 , airway support, treat acidosis, inotropes for severe early presentation
• Milder forms may present later but still with significant shock
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Congestive Heart Failure
• Presents more gradually, beyond neonatal period
• Symptoms vague – poor feeding, wt. gain etc.
• + murmurs usually appreciated
• Two groups – pulmonary overcirculation, most common
• Ventricular failure, less common
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Pulm Overcirculation
• Mod to large VSD
• AVC or AV septal defect
• Large PDA
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Overcirculation
• Signs of CHF
• PVR falls, pulmonary blood flow increases
• + murmur
• CXR – large heart, pulm edema
• Airway support, diuretics, afterload reduction surgical repair
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VSD
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PDA
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Ventricular Failure
• Anomalous left coronary artery
• Myocarditis
• Cardiomyopathies
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Anomalous Left
• Coronary Artery originates from the pulmonary artery
• PVR falls
• Steal as blood actually flows retrograde from coronary circulation to pulmonary circ
• Severe shock, ischemic myocardium
• Increase PVR, volume to perfuse heart
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Myocarditis/Cardiomyopathy
• Poor feeding, pallor, tachypnea, sweating
• Shock
• Hepatomegaly
• Cardiomegaly, increased pulmonary markings
• Milder inotrope, afterload reduction, diuresis
• Severe need intubation
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Cardiomyopathy
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