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2/27/19 1 TALES FROM THE COMMUNITY PEM DEPT: SCARY CASES! Solomon Behar, MD, FAAP, FACEP March 2, 2019

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Page 1: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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TALES FROM THE COMMUNITY PEM DEPT:

SCARY CASES!

Solomon Behar, MD, FAAP, FACEP

March 2, 2019

Page 2: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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OBJECTIVES

v Understand the ddx and management of abdominal masses in kids

v Understand strategies for dealing with the patient in refractory

status epilepticus and alternate routes of giving AEDs

v Discuss the ddx of torticollis in children

v Discuss the ddx and management of UGI bleeding in kids

A HAIRY SITUATION

Page 3: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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4 YR F LEFT SIDED ABDOMINAL MASS

v  No V/D, some hard BMs, no blood, normal UOP/quality,

v  No weight loss or “B” symptoms , “picky eater”

v  PMHx: Fe deficiency

v  AF, Normal VS

v  Normal exam except for firm LUQ mass

v  Labs: WBC 6.1, Hgb 7.8 (MCV 67), Plt 623

v  Normal renal function, UA

DDX ABDOMINAL MASS IN KIDS

v Age

•  Infants: think RENAL, MALIGNANCY •  Young kids: RENAL, POOP, HSM, MALIGNANCY •  Older kids: POOP, HSM, MALIGNANCY

v Location

v Associated symptoms:

•  fever, weight loss, hematuria, HTN, vomiting, blood in stool?

Page 4: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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MALIGNANT MASSES

v Wilm’s Tumor •  MC primary renal tumor •  Asymptomatic abdominal mass •  Hematuria, pain, vomiting,

HTN •  WAGR syndrome

•  Aniridia •  GU anomalies •  MR

•  Hemihypertrophy •  Peak age 2-3 yrs

MALIGNANT MASSES

v Neuroblastoma •  Ill appearing •  Horner’s syndrome, •  Opsoclonus-

myoclonus •  Hoarseness, •  Periorbital ecchymosis •  Elevated HVA, VMA

in urine •  90% dx before age 5

yrs

Page 5: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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YOUNGER/SLOWER GROWINGà

more likely benign

OLDER/FASTER GROWINGà

more likely malignant

WORK-UP

v UA, check BP

v CBC, CMP, tumor lysis labs •  infectious work-up?, tumor markers?

v  Imaging: KUB/US to start

Page 6: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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TRICHOBEZOAR= RAPUNZEL SYNDROME

Page 7: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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SICK IN THE HEAD

8 MOS F EMS’D IN FOR SEIZURE

v  60” GTC refractory to therapy

v T 101.2, HR 200’s, vomiting orange x4 during resusc

v  Pupils big and equal, intermittent vocalizing

v  Small rhinorrhea today

v Mom lives in motel with baby

v No home meds, no TB contacts

Page 8: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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WHAT WOULD YOU GIVE?

v  Benzos

v  Fos-phenytoin

v  Leviteracetam

v  (phenobarbital)

v  Dextrose

v  Pyridoxine

v  Abx?

IN midazolam (0.2mg/kg) PR diazepam (0.5 mg/kg, max 20mg)

Alternate routes?

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Page 10: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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Page 11: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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PAIN IN THE NECK

2 ½ Y R OLD F WON’T M OVE NECK, FE V E R , A N D PH O TO PH O BI A

v  Started with cough, URI, sore throat starting 4-5 d ago

v  Mom thought “she slept funny”

v  Febrile to 102.5, fussy, torticollis to right

v  Refused to move neck, mental status ok, ?photophobia

v  2-3+ tonsils, red OP, uvula midline. Mouth closed, refusing PO

v  Cervical LAD R>L

v  No stridor

Page 12: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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DDX?

v Meningitis

v Lymphadenitis

v Bad pharyngitis

v RPA

v Epidural abscess

v Dystonia

WORK-UP?

v WBC 18.9, left shift

v CRP: elevated

v LP:

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RETROPHARYNGEAL ABSCESS

v Age < 6 yrs

v Polymicrobial

v ENT consult STAT

v IV antibiotics +/- OR

BE CAREFUL WHAT YOU WISH FOR…

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13 YO M MRCP, AUTISM, BREAKTHROUGH SEIZURE

v BIB EMS, not seizing

v Afebrile, HR 160’s, BP ok

v  Pale but awake

v No bruising or petechiae

v No recent illness, but “not acting himself ” x2 weeks

WHY YOU NEED TO DO COMPLETE PHYSICALS

Page 16: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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Normal coags , normal LFT’s

Page 17: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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v Epistaxis**

v  PUD/H Pylori

v Esophagitis/GER

v  FB, esp button battery

v Caustic ingestion

v Medications (NSAIDs)

UGI BLEEDING IN KIDS: DDX

v Coagulopathy

v Mallory-Weiss

v  Pulm HTN/varices

v Vascular lesions/polyps

v  IBD (Crohn’s)

VIT K!

MANAGEMENT

v Resuscitate with IVF’s

v  pRBC’s/FFP if HD unstable, Hgb <8

v  Start PPI (1 mg/kg)

v  If variceal source, octreotide (1mcg/kg bolus, 1-2 mcg/kg/hr gtt)

v Emergent endoscopy or OR

v  ??? NG lavage???

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Page 19: Solomon Behar, MD, FAAP, FACEP - aapca2.orgaapca2.org/wp-content/uploads/2019/02/Breakout-2.-Behar-Interesting-Cases.pdf · v LP: 2/27/19 13 2/27/19 14 RETROPHARYNGEAL ABSCESS vAge

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DR. DANNY CHOI

SEE YOU IN THE LBC! HAPPY HALLOWEEN

Thank you!