rmt klsf dr blondina 2009
DESCRIPTION
rheumaticTRANSCRIPT
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CLASSIFICATION OF RHEUMATIC DISEASE
Blondina Marpaung
Rheumatic Division Department of Internal Medicine FK USU - Medan
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Classification of Rheumatic Disease( American Rheumatism Association 1973)
I. Diffuse Connective Disease
A. Rheumatoid Arthritis
B. Juvenile Arthitis:1. Onset systemic
2. Onset polyarticular
3. Onset Oligoarticular
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C. Systemic Lupus Eritematosus
D. Progressive Systemic Sclerosis
E. Polymyositis / dermatomyositis
F. Vasculitis nekrotisasi and another vasculopathy 1. Polyartheritis nodosa related Hepatitis B and granulomatosis alergic Churg-Strauss 2. Hypersensitivity vasculitis : Henoch Schonlein purpura.
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3. Wegener Granulomatosis 4. Giant cell arthritis a. Temporary Arthritis b. Takayasu Arthritis
5. Lymph node mucocutaneous syndrome (Kawasaki Disease)
6. Behcet Disease
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G. Sjogren Syndrome
H. Unclassifed syndrome (including mixed connective disease ).
I. Another classified :
rheumatic polymialgia ,
paniculitis (Weber-Christian disease),
erythema nodosum,
policondritis , etc.
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II. Arthitis related spondyltis
A. Ankylosing spondyltis B. Reiter syndrome C. Psoriatik arthritis D. Arthritis related chronic collitis
III. Degenerative Joint Disease (Osteoarthritis / Osteoarthrosis )
A. Primary B. Secondary
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IV. Arthritis, tenosinovyitis and bursitis related with infectionA. Direct 1. Bacteriaa. Gram positive Coccus (staphylococcus and another bacteria).b. Gram negative Cocus (gonococcus and another bacteria).c. Gram negative basild. Mycobacteriume. Treponema f. Etc
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2. Virus 3. Fungi 4. Parasite 5. Idiopathic ( Whipple Disease )
B. Indirect
Bacteria including : acute rheumatic fever, intestinal shunt, Post shigella dysentri, yersinia, etc
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V. Rheumatic disease related systemic disease and endocrin
A. Crystal influence
1. Monosodium Crystal ( gouthy ) 2. Kalsium pirofosfat dihidrat (Pseudogout, kondrokalsinosis)
3. Hidroksiapatit
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B. Biochemistry Abnormality
1. Amiloidosis 2. Vitamin C Deficiency( Scurvy ). 3. Specific enzyme deficiency :Fabry DiseaseFarber DiseaseAlkaptonuria Lesch Nyhan Syndrome 4. Dyslipidemia
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5. Mukopolisakarida 6. Haemoglobinopathy Sickle Cell disease, etc 7. Pure Connective Disorder: Ehler-Danlos SyndromeMarfan SyndromeElastic pseudo xantoma,etc 8. Etc
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C. Endocrin Disease
1. Diabetes Mellitus 2. Acromegali3. Hiperparatiroidism4. Thyroid Disease (hyperthyroidism, hypothyroidism).
D. Immunodeficiency Syndrome.
E. Another Heredity disease :.
1. Arthrogryposis multiplex congenital 2. Hypermobility Syndrome 3. Progressive Myositis Ossificans
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VI. Neoplasma.
A. Primary ( sinovioma, sinovio sarcoma ) B. Metastatic
VII.Neuropatic Disorder
A. Charcot Joint B. Compression Neuropathy 1. Peripheral entrapment (carpal-tunnel syndrome, etc) 2. Radiculopathy 3. Spinal Stenosis C. Sympathic reflex dystrophy D. Etc
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VIII. Related with bone disorder and joint manifestation
A. Osteoporosis 1. Generaly 2. Regional ( local )
B. Osteomalasia
C. Osteoartropathy hypertrofik
D. Hiperostosis skeletal idiopatik difus, including Forrestier hiperostosis disease, vertebra ankilosing
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E. Osteoitis1. Generaly osteoitis deformans - Paget disease2. Local osteoitis condensans illii, osteoitis pubis F. Necrosis avaskularG. Osteocondritis ( osteo chondritis dissecans )H. Congenital Hip Dysplasia. I. Slipped capital Femoral epiphysis.J. Costocondritis ( including Tietze syndrome )K. Osteolysis and condrolysis
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III.Nonarticular Rheumatism
A. Miofasial Pain Syndrome : 1. General: - Fibrosis - Fibriomyalgia 2. Regional.
B. Low Back Pain and discus intervertebra disorder.
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C. Tendinitis ( tenosinovitis ) and or bursitis.
1. Bursitis subakromial / subdeltoid. 2. Tenosinovytis, tendinitis bicipital. 3. Bursitis olecranon. 4. Epicondilitis humeral medial or lateral. 5. Tenosinovyitis De Quervain. 6. Capsulitis adhesif shoulder joint (frozen - shoulder) 7. Trigger finger.
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D. Ganglion CystE. Fascilitis.F. Chronic strain ligament and muscle
G. Vasomotor Disorder. 1. Erythromelalgia. 2. Raynaud Phenomen.
H. Another pain syndrome including weather sensiivity., psikogenik rheumatism
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X. Another Disorder
A. Disorder related with arthritis. 1.Trauma ( direct trauma ). 2. Lyme arthritis. 3. Pancreas Disease. 4. Sarcoidosis. 5. Palindromic Rheumatism. 6. Sinovytis villonodular. 7. Hidrartrosis intermitten. 8. Hemofilia.
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B. Another situation.
1. Internal dearrangement from joint including - condromalasia patella,- loose bodies 2. Familial mediterranean fever. 3. Eosinophilic fascilitis. 4. Active Chronic Hepatitis. 5. Drug related syndrome.
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Thank YouDr. Blondina Marpaung, SpPD - KR
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