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  • CLASSIFICATION OF RHEUMATIC DISEASE

    Blondina Marpaung

    Rheumatic Division Department of Internal Medicine FK USU - Medan

  • Classification of Rheumatic Disease( American Rheumatism Association 1973)

    I. Diffuse Connective Disease

    A. Rheumatoid Arthritis

    B. Juvenile Arthitis:1. Onset systemic

    2. Onset polyarticular

    3. Onset Oligoarticular

  • C. Systemic Lupus Eritematosus

    D. Progressive Systemic Sclerosis

    E. Polymyositis / dermatomyositis

    F. Vasculitis nekrotisasi and another vasculopathy 1. Polyartheritis nodosa related Hepatitis B and granulomatosis alergic Churg-Strauss 2. Hypersensitivity vasculitis : Henoch Schonlein purpura.

  • 3. Wegener Granulomatosis 4. Giant cell arthritis a. Temporary Arthritis b. Takayasu Arthritis

    5. Lymph node mucocutaneous syndrome (Kawasaki Disease)

    6. Behcet Disease

  • G. Sjogren Syndrome

    H. Unclassifed syndrome (including mixed connective disease ).

    I. Another classified :

    rheumatic polymialgia ,

    paniculitis (Weber-Christian disease),

    erythema nodosum,

    policondritis , etc.

  • II. Arthitis related spondyltis

    A. Ankylosing spondyltis B. Reiter syndrome C. Psoriatik arthritis D. Arthritis related chronic collitis

    III. Degenerative Joint Disease (Osteoarthritis / Osteoarthrosis )

    A. Primary B. Secondary

  • IV. Arthritis, tenosinovyitis and bursitis related with infectionA. Direct 1. Bacteriaa. Gram positive Coccus (staphylococcus and another bacteria).b. Gram negative Cocus (gonococcus and another bacteria).c. Gram negative basild. Mycobacteriume. Treponema f. Etc

  • 2. Virus 3. Fungi 4. Parasite 5. Idiopathic ( Whipple Disease )

    B. Indirect

    Bacteria including : acute rheumatic fever, intestinal shunt, Post shigella dysentri, yersinia, etc

  • V. Rheumatic disease related systemic disease and endocrin

    A. Crystal influence

    1. Monosodium Crystal ( gouthy ) 2. Kalsium pirofosfat dihidrat (Pseudogout, kondrokalsinosis)

    3. Hidroksiapatit

  • B. Biochemistry Abnormality

    1. Amiloidosis 2. Vitamin C Deficiency( Scurvy ). 3. Specific enzyme deficiency :Fabry DiseaseFarber DiseaseAlkaptonuria Lesch Nyhan Syndrome 4. Dyslipidemia

  • 5. Mukopolisakarida 6. Haemoglobinopathy Sickle Cell disease, etc 7. Pure Connective Disorder: Ehler-Danlos SyndromeMarfan SyndromeElastic pseudo xantoma,etc 8. Etc

  • C. Endocrin Disease

    1. Diabetes Mellitus 2. Acromegali3. Hiperparatiroidism4. Thyroid Disease (hyperthyroidism, hypothyroidism).

    D. Immunodeficiency Syndrome.

    E. Another Heredity disease :.

    1. Arthrogryposis multiplex congenital 2. Hypermobility Syndrome 3. Progressive Myositis Ossificans

  • VI. Neoplasma.

    A. Primary ( sinovioma, sinovio sarcoma ) B. Metastatic

    VII.Neuropatic Disorder

    A. Charcot Joint B. Compression Neuropathy 1. Peripheral entrapment (carpal-tunnel syndrome, etc) 2. Radiculopathy 3. Spinal Stenosis C. Sympathic reflex dystrophy D. Etc

  • VIII. Related with bone disorder and joint manifestation

    A. Osteoporosis 1. Generaly 2. Regional ( local )

    B. Osteomalasia

    C. Osteoartropathy hypertrofik

    D. Hiperostosis skeletal idiopatik difus, including Forrestier hiperostosis disease, vertebra ankilosing

  • E. Osteoitis1. Generaly osteoitis deformans - Paget disease2. Local osteoitis condensans illii, osteoitis pubis F. Necrosis avaskularG. Osteocondritis ( osteo chondritis dissecans )H. Congenital Hip Dysplasia. I. Slipped capital Femoral epiphysis.J. Costocondritis ( including Tietze syndrome )K. Osteolysis and condrolysis

  • III.Nonarticular Rheumatism

    A. Miofasial Pain Syndrome : 1. General: - Fibrosis - Fibriomyalgia 2. Regional.

    B. Low Back Pain and discus intervertebra disorder.

  • C. Tendinitis ( tenosinovitis ) and or bursitis.

    1. Bursitis subakromial / subdeltoid. 2. Tenosinovytis, tendinitis bicipital. 3. Bursitis olecranon. 4. Epicondilitis humeral medial or lateral. 5. Tenosinovyitis De Quervain. 6. Capsulitis adhesif shoulder joint (frozen - shoulder) 7. Trigger finger.

  • D. Ganglion CystE. Fascilitis.F. Chronic strain ligament and muscle

    G. Vasomotor Disorder. 1. Erythromelalgia. 2. Raynaud Phenomen.

    H. Another pain syndrome including weather sensiivity., psikogenik rheumatism

  • X. Another Disorder

    A. Disorder related with arthritis. 1.Trauma ( direct trauma ). 2. Lyme arthritis. 3. Pancreas Disease. 4. Sarcoidosis. 5. Palindromic Rheumatism. 6. Sinovytis villonodular. 7. Hidrartrosis intermitten. 8. Hemofilia.

  • B. Another situation.

    1. Internal dearrangement from joint including - condromalasia patella,- loose bodies 2. Familial mediterranean fever. 3. Eosinophilic fascilitis. 4. Active Chronic Hepatitis. 5. Drug related syndrome.

  • Thank YouDr. Blondina Marpaung, SpPD - KR

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