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Rheumatic Heart Disease A National (international) Perspective Graeme Maguire Cairns Clinical School School of Medicine & Dentistry James Cook University

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Page 1: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Rheumatic Heart Disease A National (international) Perspective

Graeme Maguire Cairns Clinical School School of Medicine & Dentistry James Cook University

Page 2: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

• What is it and what causes it

• How much is around (especially in women)

• Stopping it (especially as a problem in pregnancy)

• RHD in pregnancy

Rheumatic Heart Disease A National (international) Perspective

Page 3: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What is it Group A streptococcal infection

Page 4: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What is it Acute rheumatic fever

Page 5: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What is it Rheumatic heart disease

Page 6: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What is it Rheumatic heart disease

Page 7: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What is it Rheumatic heart disease

Page 8: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What causes it

Page 9: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

What causes it

Page 10: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Under the right conditions a proportion of people in any population can be at risk of ARF/RHD

Page 11: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry
Page 12: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry
Page 13: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Population at risk

GAS colonization

GAS pharyngitis

ARF

RHD

Page 14: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Population at risk

GAS colonization

GAS pharyngitis

ARF

RHD

Page 15: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

02000400060008000

1000012000140001600018000

Burden of disease (years of life lost (YLL) + years of life of disability (YLD) - Aboriginal &

Torres Strait Islander peoples - 2003

How much is around?

Page 16: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

• Extremely rare overall

BUT •Aboriginal and Torres Strait Islander children (5-14 yo) highest documented rates in the world 250-300/100 000/yr (one case for every 300 kids every year)

• ½ million cases of ARF/yr globally

How much is around? Acute rheumatic fever

Page 17: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

• Extremely rare overall BUT

• 1-2% of Aboriginal and Torres Strait Islander peoples

• 16 million people living with RHD globally

How much is around? Rheumatic heart disease

Page 18: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

0

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0 - 10 10 - 20 20 - 30 30 - 40 40 - 50 50 - 60 60 -70 70 -80 80 - 90

% o

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Age group (yrs)

FEMALES

MALES

How much is around? Rheumatic heart disease

Page 19: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

How much is around? Why more in women?

0%

10%

20%

30%

40%

50%

60%

70%

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90%

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0 - 10 10 - 20 20 - 30 30 - 40 40 - 50 50 - 60 60 -70 70 -80 80 - 90 ALL

% o

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FEMALES

• More GAS infection

• Accelerated disease

• Greater diagnosis/access

Page 20: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Because ARF/RHD is preventable and the consequences can be

severe

So why do we worry about a relatively rare condition?

Page 21: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry
Page 22: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Population at risk

GAS colonization

GAS pharyngitis

ARF

RHD

Stopping it

Page 23: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Stopping it

Population at risk

GAS colonization

GAS pharyngitis

ARF

RHD

Page 24: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Stopping it

• RHD is rarely a reason for not getting pregnant BUT planning (and possibly treatment) before pregnancy is the key

• Preventing it – primary and secondary prevention

• Fertility planning/contraceptive advice in women with RHD is EVERYONE’S business

Page 25: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

• What is it and what causes it

• How much is around (especially in women)

• Stopping it (especially as a problem in pregnancy)

• RHD in pregnancy

Rheumatic Heart Disease A National (international) Perspective

Page 26: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry
Page 27: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

Why’s it important to you?

Page 28: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry
Page 29: Rheumatic Heart Disease - RANZCOG · Rheumatic Heart Disease . A National (international) Perspective . Graeme Maguire . Cairns Clinical School . School of Medicine & Dentistry

How much is around? Rheumatic heart disease

0%

10%

20%

30%

40%

50%

60%

70%

80%

90%

100%

0 - 10 10 - 20 20 - 30 30 - 40 40 - 50 50 - 60 60 -70 70 -80 80 - 90 ALL

% o

f A

RF/

RH

D p

atie

nts

Age group (yrs)

MALES

FEMALES