partial situs abdominus with partial duodenal obstruction

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    HAYSSAM RASHWAN

    PEDIATRIC SURGERY

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    An 10-day-old male, who weighed 3 kg onpresentation, was admitted for biliousvomiting since the age of 3 days. Parentsreport a rarefaction of stool. No antenatalultrasound available.

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    Physical examination: Lax ,non distended abdomen

    Greenish vomitus

    Normal placed apex beat on left side Liver palpated on right side

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    Radiography: Plain X ray revealed dilated stomach with

    deviation of the nasogatric to the right.

    Gastrographin study revealed dilated rightsided stomach and left sided duodenum withpassage of dye in delayed film.

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    stomachduodenum

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    The intraoperative findings consisted ofduodenal obstruction due to incompleteintraluminal diaphragm of duodeno-jejunal

    junction; right sided liver; right sided

    polysplenia and stomach . Multiple spleenswere found along greater curvature.

    Normally situated colon with right sided caecumand no malrotation detected.

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    stomach

    Caecu

    m

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    polysplenia

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    diaphragm

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    Postoperative course was uneventful; thepatient tolerated breastfeeds fourth daypostoperative was discharged five days aftersurgery.

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    DD: SITUS INVERSUS TOTALIS

    MOMS

    DEXTROGASTRIA SITUS INVERSUS PARTIALIS (HETEROTAXIA)

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    Combination of partial situs inversus,polysplenia with duodenal obstruction.

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    Abdominal situs inversus carries a significantmortality because the majority of cases (95 %)have associated cardiac and splenic defects.

    A review of all cases reported in the Englishliterature confirms in addition the presence ofsignificant gastro-intestinal pathologies,mainly annular pancreas, midgut volvulusand duodenal atresia.

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    We report on an additional case ofabdominal situs inversus without cardiacabnormality, who had partial duodenalobstruction secondary to a mucosal

    diaphragm.

    This seems to be the fourteenth caseassociated with duodenal obstruction and theseventh case secondary to amucosal duodenal diaphragm, to date, in thissetting.

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    To be continued