guillain barre syndrome - gbs/cidp foundation international · axon. muscle. willison hj et al....
TRANSCRIPT
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Guillain Barre Syndrome:Life after diagnosis
Dianna Quan, MDProfessor of NeurologyNeuromuscular SectionUniversity of Colorado Denver
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I have what?!!
Bulletins et mémoires de la Société des Médecins des Hôpitaux de Paris 1916;40:1462-70
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Why me?
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What kind of GBS do I have?
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Demyelinating vs Axonal
Myelin
Axon
Muscle
Willison HJ et al. Guillain–Barre syndrome. Lancet 2016;388:717-727
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Demyelinating vs Axonal
antibody
Willison HJ et al. Guillain–Barre syndrome. Lancet 2016;388:717-727
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What kind of GBS do I have?
• Acute inflammatory demyelinating polyneuropathy (AIDP)• Acute motor axonal neuropathy (AMAN)• Acute motor sensory axonal neuropathy (AMSAN)• Miller Fisher Syndrome (MFS)• Other localized forms reported
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What now?normal
nadir
recovery
time
function
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How is GBS treated?normal
nadir
recovery
time
functiontreatment
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Plasma exchange and IV immunoglobulin (IVIG)normal
nadir
recovery
time
functiontreatment
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How do plasma exchange and IVIG work?
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Will I get better? And When?
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Can I do anything to get better faster?
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Can I do anything to get better faster?
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Will it happen again?
• Probably not• Chances of various things happening
• Getting GBS again: 1-5/100 who had GBS once• Dying from cancer: 1/7• Dying in a car crash: 1/100• Dying of a heart attack: 1/6
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