guidelines for the diagnosis and treatment of pulmonary hypertension by, nazzareno galiè, marius m....

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Guidelines for the diagnosis and treatment of pulmonary hypertension by , Nazzareno Galiè, Marius M. Hoeper, Marc Humbert, Adam Torbicki, Jean-Luc Vachiery, Joan Albert Barbera, Maurice Beghetti, Paul Corris, Sean Gaine, J. Simon Gibbs, Miguel Angel Gomez-Sanchez, Guillaume Jondeau, Walter Klepetko, Christian Opitz, Andrew Peacock, Lewis Rubin, Michael Zellweger, Gerald Simonneau, , Alec Vahanian, Angelo Auricchio, Jeroen Bax, Claudio Ceconi, Veronica Dean, Gerasimos Filippatos, Christian Funck-Brentano, Richard Hobbs, Peter Kearney, Theresa McDonagh, Keith McGregor, Bogdan A. Popescu, Zeljko Reiner, Udo Sechtem, Per Anton Sirnes, Michal Tendera, Panos Vardas, Petr Widimsky, , Udo Sechtem, Nawwar Al Attar, Felicita Andreotti, Michael Aschermann, Riccardo Asteggiano, Ray Benza, Rolf Berger, Damien Bonnet, Marion Delcroix, Luke Howard, Anastasia N Kitsiou, Irene Lang, Aldo Maggioni, Jens Erik Nielsen-Kudsk, Myung Park, Pasquale Perrone- Filardi, Suzanna Price, Maria Teresa Subirana Domenech, Anton Vonk-Noordegraaf, and Jose Luis Zamorano EHJ Volume 30(20):2493-2537 October 14, 2009 © The European Society of Cardiology 2009. All rights reserved. For permissions please email: [email protected]

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Page 1: Guidelines for the diagnosis and treatment of pulmonary hypertension by, Nazzareno Galiè, Marius M. Hoeper, Marc Humbert, Adam Torbicki, Jean-Luc Vachiery,

Guidelines for the diagnosis and treatment of pulmonary hypertension

by , Nazzareno Galiè, Marius M. Hoeper, Marc Humbert, Adam Torbicki, Jean-Luc Vachiery, Joan Albert Barbera, Maurice Beghetti, Paul Corris, Sean Gaine, J. Simon

Gibbs, Miguel Angel Gomez-Sanchez, Guillaume Jondeau, Walter Klepetko, Christian Opitz, Andrew Peacock, Lewis Rubin, Michael Zellweger, Gerald

Simonneau, , Alec Vahanian, Angelo Auricchio, Jeroen Bax, Claudio Ceconi, Veronica Dean, Gerasimos Filippatos, Christian Funck-Brentano, Richard Hobbs, Peter Kearney, Theresa McDonagh, Keith McGregor, Bogdan A. Popescu, Zeljko

Reiner, Udo Sechtem, Per Anton Sirnes, Michal Tendera, Panos Vardas, Petr Widimsky, , Udo Sechtem, Nawwar Al Attar, Felicita Andreotti, Michael Aschermann,

Riccardo Asteggiano, Ray Benza, Rolf Berger, Damien Bonnet, Marion Delcroix, Luke Howard, Anastasia N Kitsiou, Irene Lang, Aldo Maggioni, Jens Erik Nielsen-

Kudsk, Myung Park, Pasquale Perrone-Filardi, Suzanna Price, Maria Teresa Subirana Domenech, Anton Vonk-Noordegraaf, and Jose Luis Zamorano

EHJVolume 30(20):2493-2537

October 14, 2009

© The European Society of Cardiology 2009. All rights reserved. For permissions please email: [email protected]

Page 2: Guidelines for the diagnosis and treatment of pulmonary hypertension by, Nazzareno Galiè, Marius M. Hoeper, Marc Humbert, Adam Torbicki, Jean-Luc Vachiery,

Diagnostic algorithm.

Authors/Task Force Members et al. Eur Heart J 2009;30:2493-2537

© The European Society of Cardiology 2009. All rights reserved. For permissions please email: [email protected]

Page 3: Guidelines for the diagnosis and treatment of pulmonary hypertension by, Nazzareno Galiè, Marius M. Hoeper, Marc Humbert, Adam Torbicki, Jean-Luc Vachiery,

Evidence-based treatment algorithm for pulmonary arterial hypertension patients (for group 1 patients only). *To maintain arterial blood O2 pressure ≥8 kPa (60 mmHg). †Under regulatory review in the European Union. §IIa-C for WHO-FC II. APAH = associated pulmonary arterial

hypertension; BAS = balloon atrial septostomy; CCB = calcium channel blocker; ERA = endothelin receptor antagonist; IPAH = idiopathic pulmonary arterial hypertension; PDE5 I = phosphodiesterase type-5 inhibitor; WHO-FC = World Health Organization functional class.

Authors/Task Force Members et al. Eur Heart J 2009;30:2493-2537

© The European Society of Cardiology 2009. All rights reserved. For permissions please email: [email protected]