endokrinuli sistemis, kvebisa da nivtierebata cvlis ... · ginekomastia (n 62) e hipoparatireozi ar...

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184 avadmyofobaTa saerTaSoriso klasifikacia Tavi IV. endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani (E00-E90) SeniSvna: simsivneebi (funqciurad aqtiuri Tu ara aqtiuri) Setanilia II klasSi. am klasSi Semavali Sesabamisi kodebi (magaliTad, E05.8, E07.0, E16-E31,E34.) aucileblobis (saWiroebis) SemTxvevaSi SeiZleba gamoyenebuli iyos, rogorc damatebiTi (kodebi) funqciurad aqtiuri simsivneebisa da eqtopiuri endokrinuli qsovilebis da, agreTve, sxva rubrikebSi Setanil simsivneebTan da sxva paTologiebTan dakavSirebuli endokrinuli jirkvlis hiper- da hipofunqciis aRsaniSnavad. ar igulisxmeba: orsulobis, mSobiarobis da loginobis xanis garTulebani (O00-O09) klinikuri da laboratoriuli gamokvlevebiT gamovlenili simptomebi, niSnebi da normidan gadaxrebi, romlebic ar aris Setanili sxva rubrikebSi (R00-R99) nayofisa da axalSobilis endokrinuli funqciebisa da nivTierebaTa cvlis gardamavali specifikuri darRvevebi (P70-P74) es klasi Seicavs Semdeg blokebs: E00-E07 farisebri jirkvlis avadmyofobani E10-E14 Saqriani diabeti E15-E16 glukozis regulaciisa da pankreasis Sinagani sekreciis funqciis sxva darRvevebi E20-E35 sxva endokrinuli jirkvlebis avadmyofobebi E40-E46 malnutricia (sakvebis arasakmao raodenobiT miReba) E50-E64 kvebiTi deficitis sxva saxeebi E65-E68 simsuqne da sxva saxis hiperalimentaciebi da Warbi kvebis sxva saxeebi E70-E90 nivTierebaTa cvlis darRvevebi am Tavis varskvlaviani kategoriebi mocemulia Semdegi saxiT: E35* endokrinuli jirkvlebis dazianebani im avadmyofobaTa dros, romlebic Setanilia sxva klasifikaciebSi E90* kvebisa da nivTierebaTa cvlis darRvevebi im avadmyofobaTa dros, romelicüSetanilia sxva klasifikaciebSi farisebri jirkvlis avadmyofobebi (E00-E07) Tandayolili iod-deficituri sindromi igulisxmeba: endemiuri mdgomareobani, rogorc uSualod dakavSirebuli bunebriv garemoSi arsebul iodis deficitTan da, rogorc dedis organizmSi iodis deficitis Sedegi. zogierTi aseTi mdgomareoba ar ganekuTvneba WeSmarit hipoTireozs, aramed warmoadgens ganviTarebadi nayofis organizmSi farisebri jirkvlis hormonebis araadeqvaturi sekreciis Sedegs; SeiZleba arsebobdes kavSiri Ciyvis gamomwvev bunebriv faqtorebTan. Tanmxlebi gonebrivi SezRudulobis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi kodi (F 70-F 79) ar igulisxmeba:iodis deficitiT gamowveuli subklinikuri hipoTireozi (E 02) E00

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Page 1: endokrinuli sistemis, kvebisa da nivTierebaTa cvlis ... · ginekomastia (N 62) E hipoparaTireozi ar igulisxmeba: di jorjis sindromi (D 82.1) samedicino proceduris Semdgomi hipoparaTireozi

184

avadmyofobaTa saerTaSoriso klasifikacia

Tavi IV.

endokrinuli sistemis, kvebisa da nivTierebaTa cvlis

darRveviT gamowveuli avadmyofobani

(E00-E90)

SeniSvna: simsivneebi (funqciurad aqtiuri Tu ara aqtiuri) Setanilia II klasSi. am klasSi SemavaliSesabamisi kodebi (magaliTad, E05.8, E07.0, E16-E31,E34.) aucileblobis(saWiroebis) SemTxvevaSi SeiZleba gamoyenebuli iyos, rogorc damatebiTi(kodebi) funqciurad aqtiuri simsivneebisa da eqtopiuri endokrinuliqsovilebis da, agreTve, sxva rubrikebSi Setanil simsivneebTan da sxvapaTologiebTan dakavSirebuli endokrinuli jirkvlis hi per- dahipofunqciis aRsaniSnavad.

ar igulisxmeba: orsulobis, mSobiarobis da loginobis xanis garTulebani (O00-O09)klinikuri da laboratoriuli gamokvlevebiT gamovlenili

simptomebi, niSnebi da normidan gadaxrebi, romlebic ar aris Setanili sxvarubrikebSi (R00-R99)

nayofisa da axalSobilis endokrinuli funqciebisa da nivTierebaTa cvlisgardamavali specifikuri darRvevebi (P70-P74)

es klasi Seicavs Semdeg blokebs:

E00-E07 farisebri jirkvlis avadmyofobaniE10-E14 Saqriani diabetiE15-E16 glukozis regulaciisa da pankreasis Sinagani sekreciis funqciis sxva darRvevebiE20-E35 sxva endokrinuli jirkvlebis avadmyofobebiE40-E46 malnutricia (sakvebis arasakmao raodenobiT miReba)E50-E64 kvebiTi deficitis sxva saxeebiE65-E68 simsuqne da sxva saxis hiperalimentaciebi da Warbi kvebis sxva saxeebiE70-E90 nivTierebaTa cvlis darRvevebi

am Tavis varskvlaviani kategoriebi mocemulia Semdegi saxiT:

E35* endokrinuli jirkvlebis dazianebani im avadmyofobaTa dros, romlebic Setaniliasxva klasifikaciebSi

E90* kvebisa da nivTierebaTa cvlis darRvevebi im avadmyofobaTa dros,romelicüSetanilia sxva klasifikaciebSi

farisebri jirkvlis avadmyofobebi

(E00-E07)E

Tandayolili iod-deficituri sindromi

igulisxmeba: endemiuri mdgomareobani, rogorc uSualod dakavSirebuli bunebrivgaremoSi arsebul iodis deficitTan da, rogorc dedis organizmSi iodisdeficitis Sedegi. zogierTi aseTi mdgomareoba ar ganekuTvneba WeSmarithi poTireozs, aramed warmoadgens ganviTarebadi nayofis organizmSifarisebri jirkvlis hormonebis araadeqvaturi sekreciis Sedegs; SeiZleba

arsebobdes kavSiri Ciyvis gamomwvev bunebriv faqtorebTan.Tanmxlebi gonebrivi SezRudulobis identifikaciis aucileblobis SemTxvevaSigamoiyeneba damatebiTi kodi (F 70-F 79)ar igulisxmeba:iodis deficitiT gamowveuli subklinikuri hipoTireozi (E 02)

E

E00

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185

endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E00.0 Tandayolili iod-deficituri sindromi, nevrologiuri formaendemiuri kretinizmi, nevrologiuri forma

E00.1 Tandayolili iod-deficituri sindromi, miqsedemuri formaendemuri kretinizmi:

. hipoTiroiduli

. miqsedemuri forma

E00.2 Tandayolili iod-deficituri sindromi, Sereuli tipiendemuri kretinizmi, Sereuli tipi

E00.9 Tandayolili iod-deficituri sindromi, dauzustebeliTandayolili iod-deficituri hipoTireozi, romelic sxvagvarad ar aris dazustebuli

endemurri kretinizmi, romelic sxvagvarad ar aris dazustebuli

Efarisebri jirkvlis iodis deficitTan dakavSirebuli dazianebani da

msgavsi mdgomareobani

ar igulisxmeba: Tandayolili iod-deficituri sindromi (E 00.-)subklinikuri iod-deficituri hipoTireozi (E 02)

E01.0 iodis deficitTan dakavSirebuli difuzuri (endemuri) CiyviE01.1 iodis deficitTan dakavSirebuli mravalkvanZovani (endemuri) Ciyvi

iodis deficitTan dakavSirebuli kvanZovani Ciyvi

E01.2 iodis deficitTan dakavSirebuli (endemuri) Ciyvi, dauzustebeliendemuri Ciyvi, romelic sxvagvarad ar aris dazustebuli

E01.8 iodis deficitTan dakavSirebuli farisebri jirkvlis sxva dazianebanida mdgomareobaniSeZenili iod-deficituri hipoTireozi, romelic sxvagvarad ar aris dazustebuli

E subklinikuri iod-deficituri hipoTireozi

E

hipoTireozis sxva formebi

ar igulisxmeba: iodis deficitTan dakavSirebuli hipoTireozi (E00-E02)samedicino procedurebis Semdeg ganviTarebuli hipoTireozi (E 89.0)

E03.0 Tandayolili hipoTireozi difuzuri CiyviTCiyvi (aratoqsiuri) Tandayolili:

. romelic, sxvagvarad ar aris dazustebuli

. parenqimuli

ar igulisxmeba: gardamavali Tandayolili Ciyvi normaluri funqciiT (P 72.0)E03.1 Tandayolili hipoTireozi Ciyvis gareSe

farisebri jirkvlis aplazia (miqsedemiT)

Tandayolili:. farisebri jirkvlis atrofia

. hipoTireozi, romelic sxvagvarad ar aris dazustebuli

E03.2 medikamentebiT da sxva egzogenuri nivTierebebiT gapirobebulihipoTireozi

mizezis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba garegani mizezebis

damatebiTi kodi (klasi XX)

E03.3 postinfeqciuri hipoTireoziE03.4 farisebri jirkvlis atrofia (SeZenili)

ar igulisxmeba: farisebri jirkvlis Tandayolili atrofia (E 03.1)E03.5 miqsedemuri koma

E01

E02

E03

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186

avadmyofobaTa saerTaSoriso klasifikacia

E03.8 sxva saxis dazustebuli hipoTireoziE03.9 hipoTireozi, dauzustebeli

miqsedema, romelic sxvagvarad ar aris dazustebuli

aratoqsiuri Ciyvis sxva formebi

ar igulisxmeba:Tandayolili Ciyvi:

. romelic sxvagvarad araris dazustebuli

. difuzuri (E 03.0)

. parenqimuli

iodis-deficitTan dakavSirebuli Ciyvi (E 00-E 02)E04.0 aratoqsiuri difuzuri Ciyvi

Ciyvi, aratoqsiuri:

. difuzuri, (koloiduri)

. martivi

E04.1 aratoqsiuri erTkvanZiani Ciyvikoloiduri kvanZi (cisturi)(Tireoiduli)

aratoqsiuri erTkvanZovani Ciyvi

Tireoiduli (cisturi) kvanZi, romelic sxvagvarad ar aris dazustebuli

E04.2 aratoqsiuri mravalkvanZovani Ciyvicisturi Ciyvi, romelic sxvagvarad ar aris dazustebuli

mravalkvanZovani (cisturi) Ciyvi, romelic sxvagvarad ar aris dazustebuli

E04.8 aratoqsiuri Ciyvis sxva dazustebuli formebiE04.9 aratoqsiuri Ciyvi, dauzustebeli formebi

Ciyvi, romelic sxvagvarad ar aris dazustebuli

kvanZovani Ciyvi (aratoqsiuri), romelic sxvagvarad ar aris dazustebuli

ETireotoqsikozi [hiperTireozi]

ar igulisxmeba: qronikuli Tiroiditi gardamavali TireotoqsikoziT (E 06.2)neonataluri Tireotoqsikozi (P 72.1)

E05.0 Tireotoqsikozi difuzur CiyviTegzoftalmuri an toqsiuri Ciyvi, romelic sxvagvarad ar aris dazustebuli

greivsis avadmyofoba

difuzuri toqsiuri Ciyvi

E05.1 Tireotoqsikozi farisebri jirkvliseuli toqsiuri kvanZiTTareotoqsikozi erTkvanZovani toqsiuri CiyviT

E05.2 Tireotoqsikozi mravalkvanZovani toqsiuri Ciyvitoqsinuri kvanZovani Ciyvi, romelic sxvagvarad ar aris dazustebuli

E05.3 Tireotoqsikozi, eqtopiuri Tireoiduli qsovilidanE05.4 Tireotoqsikozi xelovnuriE05.5 Tiroiduli krizi anu SetevaE05.8 Tireotoqsikozis sxva formebi

Tireo-mastimulebeli hormonis Warbi produqcia

Tu mizezis identifikaciis survili gagvT, gamoiyeneT damatebiTi garegani mizezebis kodi (Tavi XX)

E05.9 Tireotoqsikozi dauzustebelihiperTireozi, romelic sxvagvarad ar aris dazustebuli

gulis Tireotoqsinuri avadmyofoba + (I43.8*)

Tiroiditi

ar igulisxmeba: mSobiarobis Semdgomi Tiroiditi (O 90.5)

E04

E05

E06

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187

endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E06.0 mwvave Tiroiditifarisebri jirkvlis abscesi

Tiroiditi:. Cirqovani (piogenuri). supuraciuliinfeqciuri agentis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi

kodi (B 95-B 97)E06.1 qvemwvave Tiroiditi

Tireoiditi:

. de kervenis

. giganturujredovani

. granulomatozuri

. araCirqovani

ar igulisxmeba: autoimunuri Tiroiditi (E 06.3)E06.2 qronikuli Tiroiditi gardamavali TireotoqsikoziT

ar igulisxmeba: autoimunuri Tireoiditi (E 06.3)E06.3 autoimunuri Tiroiditi

haSimotos Tiroiditi

haSitoqsikozi (gardamavali)limfadenoiduri Ciyvilimfocituri Tireoiditi

limfomatozuri Ciyvi

E06.4 wamliT gamowveuli TireoiditiTu wamlis identifikaciis aucileblobis SemTxvevaSi damatebiTi garegani mizezebis kodi

(klasi XX)

E06.5 sxva saxis qronikuli TiroiditebiTiroiditi:. qronikuli. romelic sxvagvarad ar aris dazustebuli. fibrozuli. mkvrivi

. ridelis

E06.9 Tiroiditi dauzustebeliE

farisebri jirkvlis sxva avadmyofobani

EE07.0 kalcitoninis hipersekrecia

farisebri jirkvlis C-ujredebis hiperplazia

Tireokalcitoninis hipersekrecia

E07.1 dishormonuli Ciyviojaxuri dishormogenuli Ciyvi

pendredis sindromiar igulisxmeba: Tandayolili gardamavali Ciyvi farisebri jirkvlis normaluri funqciiT

(P 72.0)E07.8 farisebri jirkvlis sxva dauzustebeli avadmyofobani

farisebri jirkvlis hormonebis SemkavSirebuli globulinis paTologia

sisxlis Caqceva farisebr jirkvalSifarisebri jirkvlis infarqti

avadmyofuri euTiroiduli sindromi

E07.9 farisebri jirkvlis daavadebebi, dauzustebeli

E07

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188

avadmyofobaTa saerTaSoriso klasifikacia

Saqriani diabeti

(E10-E14)

samkurnalo preparatis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi gareganimizebis kodi (klasi XX)

qvemoT aRniSnuli meoTxe niSnebi gamoiyeneba E10 - E14 rubrikebTa erTad:

. 0 komiT

diabeturi. koma ketoacidoziT an mis gareSe. hiperosmosuri koma. hipoglikemiuri komahiperglikemiuri koma, romelic sxvagvarad ar aris dazustebuli

. 1 ketoacidoziT

diabeturi:. acidozi. ketoacidozi

. 2† Tirkmlebis dazianebiT

diabeturi nefropaTia (N 08.3*)intrakapilaruli glomerulonefrozi (N 08.3*)kimelstil-uilsonis sindromi (N 08.3*)

. 3† Tvalebis dazianebiT

diabeturi:. kataraqta (H 28.0*). retinopaTia (H 36.0*)

. 4† nevrologiuri garTulebebiT

diabeturi:. amiotrofia (G 73.0*). avtonomiuri neiropaTia (G 99.0*). mononeiropaTia (G 59.0*). polineiropaTia (G 63.2*). avtonomiuri (G 99.0*)

. 5 periferiuli cirkulaciis moSliT

diabeturi:. gangrena. periferiuli angiopaTia + (I79.2*). wyluli

. 6 sxva saxis specifikuri garTulebebiT

diabeturi arTropaTia + (M 14.2*). neiropaTiuri + (M 14.6*)

. 7 mravlobiTi garTulebebiT

. 8 dauzustebeli garTulebebiT

. 9 garTulebebis gareSe

insulindamokidebuli Saqriani diabeti

[ix. gv. 188 qvedanayofebisaTvis]

igulisxmeba: diabeti (Saqriani):. labiluri. iuvenilur asakSi. ketozisadmi midrekilebiT. tipi I

ar igulisxmeba: Saqriani diabeti:. arasakmaris kvebasTan dakavSirebuli (E 12.-). neonataluri (P 70.2). orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:

E10

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189

endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

. romelic sxvagvarad ar aris dazustebuli (R 81)

. Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)

Einsulindamoukidebeli Saqriani diabeti

[ix. gv. 188 qvedanayofebisaTvis]

igulisxmeba: diabeti (Saqriani)(simsuqnis gareSe)(simsuqniT):. dawyebuli mozrdilTa asakSi. dawyebuli mowifulobis periodSi. ketozisadmi midrekilebis gareSe. stabiluri. tipi IIaxalgazrdaTa insulindamoukidebuli diabeti

ar igulisxmeba: Saqriani diabeti:. arasakmaris kvebasTan dakavSirebuli (E 12.-). neonataluri (P 70.2). orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)

arasakmaris kvebasTan dakavSirebuli Saqriani diabeti

[ix. gv. 188 qvedanayofebisaTvis]

igulisxmeba: arasakmaris kvebasTan dakavSirebuli Saqriani diabeti:. insulindamokidebuli

. insulindamoukidebeli

ar igulisxmeba:Saqriani diabeti orsulobis, mSobiarobis dros da mSobiarobis SemdgomperiodSi (O 24.-)

glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)neonataluri Saqriani diabeti (P 70.2)

postoperaciuli hipoinsulinemia (E 89.1)

ESaqriani diabetis sxa dazustebuli formebi

[ix. gv. 188 qvedanayofebisaTvis]ar igulisxmeba: Saqriani diabeti:

. insulindamokidebuli (E 10.-)

. arasakmaris kvebasTan dakavSirebuli (E 12.-)

. neonataluri (P 70.2)

. insulindamoukidebeli (E 11.-)

. orsulobis, mSobiarobis dros da mSobiarobis Semdgom periodSi (O24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)

dauzustebeli Saqriani diabeti

E11

E12

E13

E14

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190

avadmyofobaTa saerTaSoriso klasifikacia

[ix. gv. 188 qvedanayofebisaTvis]

igulisxmeba: diabeti, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: Saqriani diabeti:

. insulindamokidebuli (E 10.-)

. arasakmaris kvebasTan dakavSirebuli (E 12.-)

. neonataluri (P 70.2)

. insulindamoukidebeli (E 11.-)

. orsulobis, mSobiarobis da mSobiarobis Semdgom periodSi (O 24.-)glukozuria:. romelic sxvagvarad ar aris dazustebuli (R 81). Tirkmlismieri (E 74.8)daqveiTebuli tolerantoba glukozis mimarT (R 73.0)postoperaciuli hipoinsulinemia (E 89.1)

glukozis regulaciisa da pankreasis Sinagani sekreciis funqciis

sxva darRvevebi

(E15-E16)E

aradiabeturi hipoglikemiuri koma

wamlismieri insulinuri koma aradiabetian avadmyofebSi

hiperinsulinizmi hipoglikemiuri komiThipoglikemiuri koma, romelic sxvagvarad ar aris dazustebuliTu wamliT gamowveulia da gsurT wamlis identifikacia, gamoiyeneT damatebiTi garemizezebis kodi (Tavi XX)

Epankreasis Sinagani sekreciis sxva darRvevebi

EE16.0 wamlismieri hipoglikemia komis gareSe

samkurnalo saSualebis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiT

gare mizezebis kodi (Tavi XX)

E16.1 hipoglikemiebis sxva formebifunqciuri ara hiperinsulinemiuri hipoglikemia

hiperinsulinizmi. romelic sxvagvarad ar aris dazustebuli. funqciuripankreasis kunZulebis beta-ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli

encelofaTia hipoglikemiuri komis Semdeg

E16.2 hipoglikemia, dauzustebeliE16.3 glukagonis gaZlierebuli sekrecia

pankreasis endokrinuli ujredebis hiperplazia glukagonis gaZlierebuli sekreciiT

E16.8 pankreasis Sinagani sekreciis sxva dazustebuli darRvevebihipergastrinemia

endokrinuli pankreasis mier gaZlierebuli sekrecia:. zrdis hormonis "rilizing hormonis". pankreasuli polipeptidis. somatostatinis. vazoaqtiuri nawlavuri polipeptidis

zolinger-elisonis sindromi

E16.9 pankreasis Sinagani sekreciis darRveva dauzustebelikunZulakebis ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli

pankreasis endokrinuli ujredebis hiperplazia, romelic sxvagvarad ar aris dazustebuli

E15

E16

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191

endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

sxva endokrinuli jirkvlebis avadmyofobebi

(E20-E35)ar igulisxmeba: galaktorea (N 64.3)

ginekomastia (N 62)

E hipoparaTireozi

ar igulisxmeba: di jorjis sindromi (D 82.1)samedicino proceduris Semdgomi hipoparaTireozi (E 89.2)tetania, romelic sxvagvarad ar aris dazustebuli (R 29.0)axalSobilTa gardamavali hipoparaTireozi (P 71.4)

E20.0 odiopaTiuri hipoparaTireoziE20.1 fsevdohipoparaTireoziE20.8 hipoparaTireozis sxva formebiE20.9 hipoparaTireozi, dauzustebeli

paraTireoiduli tetania

hiperparaTireozi da farisebraxlo jirkvlebis sxva darRvevebi

ar igulisxmeba: osteomalacia:

. mozrdilTa (M 83.-)

. bavSvTa da mozardTa (E 55.0)E21.0 pirveladi hiperparaTireozi

farisebraxlo jirkvlebis hiperplazia

generalizebuli fibrozuli cisturi ostiti [fon reklinhauzenis Zvlis avadmyofoba]

E21.1 meoradi hiperparaTireoidozi, romelic ar aris Setanili sxva klasifikaciebSiar igulisxmeba: Tirkmlismieri warmoSobis meoradi hiperparaTireozi (N 25.8)

E21.2 hiperparaTireozis sxva formebiar igulisxmeba:ojaxuri hipokalciuriuli hiperkalciemia (E 83.5)

E21.3 hiperparaTireozi, dauzustebeliE21.4 farisebraxlo jirkvlebis sxva dazustebuli avadmyofobebiE21.5 farisebraxlo jirkvlebis avadmyofoba, dauzustebeliE

hipofizis hiperfunqcia

ar igulisxmeba: kuSingis sindromi (E 24.-)nelsonis sindromi (E 24.1)Warbi produqcia:. adenokortikotropuli (akth)-is, romelic ar aris dakavSirebuli

kuSingis avadmyofobasTan (E 27.0). hipofizis akth-is (E 24.0). Tiroid-mastimulaciebuli hormonis (E 05.8)

E22.0 akromegalia da hipofizuri gigantizmiakromegaliasTan dakavSirebuli arTropaTia +(M 14.5*)zrdis hormonis Warbi produqciaar igulisxmeba: konstituciuri:

. gigantizmi (E 34.4)

. maRali tani (E 34.4)endokrinuli pankreasis mier zrdis hormonis "rilizingiz hormonis" gaZlierebuli sekrecia (E 16.8)

E22.1 hiperprolaqtinemiahiperprolaqtinemiis gamomwvevi samkurnalo saSualebis identifikaciis aucileblobis

SemTxvevaSi gamoiyeT gare mizezebis kodi (Tavi XX)

E20

E21

E22

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avadmyofobaTa saerTaSoriso klasifikacia

E22.2 antidiurezuli hormonis araadeqvaturi sekreciis sindromiE22.8 hipofizis hiperfunqciebis sxva mdgomareobani

centraluri warmoSobis naadrevi sqesobrivi momwifeba

E22.9 hipofizis hiperfunqcia dauzustebeli

E hipofizis hipofunqcia da sxva darRvevebi

igulisxmeba: qvemoCamoTvlili mdgobareobani, miuxedavad imisa, dazianeba hipofizSiaTu hipoTalamusSi

ar igulisxmeba:procedurebis Semdeg aRmocenebuli hipopituitarizmi (E 89.3)E23.0 hipopituitarizmi

fertiluri evnuxoiduri sindromi

hipogonadotropuli hipogonadizmizrdis hormonis idiopaTiuri deficitiizolirebuli deficiti:. gonadotropinis

. zrdis hormonis

. hipofizis sxva hormonebis

kalmanis sindromilorein-levis dabali aRnagoba {qondriskacoba]hipofizis nekrozi (mSobiarobis Semdgomi)panhipopituitarizmihipofizuri:. kaxeqsia. ukmarisoba, romelic sxvagvarad ar aris dazustebuli. dabali tani (qondriskacoba). Sihenis sindromi

. simondsis avadmyofoba

E23.1 wamlismieri hipopituitarizmiwamlis identifikaciis aucileblobis SemTxvevaSi gamoiyeneba damatebiTi gare mizezebis

kodi (Tavi XX)

E23.2 uSaqro diabetiar igulisxmeba: nefrogenuli uSaqro diabeti (N 25.1)

E23.3 hipoTalamusis disfunqcia, romelic ar aris Setanili sxva klasifikaciebSiar igulisxmeba: prader-vilis sindromi (Q 87.1)

rasel-silveris sindromi (Q 87.1)E23.6 hipofizis sxva dazianebebi

hipofizis abscesi

adipozogenitaluri distrofia

E23.7 hipofizis dazianeba dauzustebeliE

kuSingis sindromi

EE24.0 hipofiz-damokidebuli kuSingis avadmyofoba

hipofizis akth-is Warbi produqcia

hipofiz-damokidebuli hiperadrenokorticizmi

E24.1 nelsonis sindromiE24.2 wamlismieri kuSingis sindromi

samkurnalo saSualebis identifikaciis SemTxvevaSi gamoiyeneba damatebiTi gare mizezebis

kodi (Tavi XX)

E24.3 eqtopiuri akth - sindromiE24.4 alkoholiT gamowveuli fsevdo-kuSingis sindromi

E23

E24

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E24.8 sxva saxis kuSingis sindromiE24.9 kuSingis sindromi dauzustebeli

adrenogenitaluri darRvevebi

igulisxmeba:adrenogenitaluri sindromebi, virilizacia an feminizacia, SeZenili angapirobebuli Tirkmelzeda jirkvlis hiperplaziiT, romelicwarmoadgens hormonTa sinTezisaTvis aucilebeli fermentebis Tandayoliliukmarisobis Sedegs

qalis:. Tirkmelzeda jirkvlismieri fsevdohermafroditizmi. heteroseqsualuri naadrevi cru sqesobrivi momwifebamamakacis:

. izoseqsualuri naadrevi cru sqesobrivi momwifeba

. naadrevi makrogenitosomia prde cox (adreuli)

. naadrevi sqesobrivi momwifeba Tirkmelzeda jirkvlis hiperplaziiT

virilizacia (qalis)

E25.0 fermentebis deficitTan dakavSirebuli Tandayolili adrenogenitaliuridarRvevebiTirkmelzeda jirkvlebis Tandayolili hiperplazia21-hidroqsilazis deficiti

marilebis-kargviT mimdinare Tirkmelzeda jirkvlebis Tandayolili hiperplazia

E25.8 sxva adrenogenitaluri darRvevebiidiopaTiuri adrenogenitaliuri darRveva

Tu wamliT gamowveulia da wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare

mizezebis kodi (Tavi XX)

E25.9 adrenogenitaliuri moSliloba, dauzustebeliadrenogenitaliuri sindromi, romelic sxvagvarad ar aris dazustebuli

Ehiperaldosteronizmi

EE26.0 pirveladi hiperaldosteronizmi

konis sindromi

pirveladi aldosteronizmi, gamowveuli Tirkmelzeda jirkvlebis ormxrivi hiperplaziiT

E26.1 meoradi hiperaldosteronizmiE26.8 sxva saxis hiperaldosteronizmi

barteris sindromi

E26.9 hiperaldosteronizmi, dauzustebeliE

Tirkmelzeda jirkvlis sxva darRvevebi

EE27.0 sxva adrenokortikuli zeaqtivoba

akth-is Warbi produqcia, romelic ar aris dakavSirebuli kuSingis avadmyofobasTan

ar igulisxmeba: kuSingis sindromi (E 24.-)E27.1 pirveladi adrenokortikuli ukmarisoba

adisonis avadmyofoba

autoimunuri adrenalitiar igulisxmeba: amiloidozi (E 85.-)

adisonis tuberkulozuri avadmyofoba (A 18.7)vaterpauz-frideriksenis sindromi (A 39.1)

E27.2 adisonuri krizi

E25

E26

E27

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avadmyofobaTa saerTaSoriso klasifikacia

Tirkmelzeda jirkvlismieri krizi

adrenokortikuli krizi

E27.3 wamlismieri adrenokortikuli ukmarisobaTu wamlis identifikacia gsurT, isargebled damatebis gare mizezTa kodiT (Tavi XX)

E27.4 sxva da dauzustebeli adrnokortikuli ukmarisobaTirkmelzeda jirkvlis:

. sisxlCaqceva

. infarqtiadrenokortikuli ukmarisoba, romelic sxvagvarad ar aris dazustebulihipoaldosteronizmiar igulisxmeba: adrenoleikodistrofia (adison-Silteris)(E 71.3)

vaterhauz-fridriksenis sindromi (A 39.1)E27.5 Tirkmelzeda jirkvlis tvinovani Sris hiperfunqcia

Tirkmelzeda jirkvlis tvinovani Sris hiperplazia

kateqolaminebis hipersekrecia

E27.8 Tirkmelzeda sxva dazustebuli darRvevebikortizol-SemboWveli globulinis paTologia

E27.9 Tirkmelzeda jirkvlis funqciis darRveva, dauzustebeli

E sakvercxeebis disfunqcia

ar igulisxmeba: gonadotropinis izolaciuri deficiti (E 23.0) sakvercxis postproceduruli dazianeba (E 89.4)

E28.0 estrogenis siWarbeTu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa

kodiT (Tavi XX)

E28.1 androgenis siWarbesakvercxis androgenebis hipersekrecia

Tu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa

kodiT (Tavi XX)

E28.2 polikisturi sakvercxis sindromisklerokistuli sakvercxis sindromi

Stein-leventalis sindromi

E28.3 sakvercxis pirveladi ukmarisobaestrogenebis daqveiTebuli raodenoba

naadrevi menopauza, romelic sxvagvarad ar aris dazustebulirezistentuli sakvercxis sindromiar igulisxmeba: menopauzuri da qalTa klimaqsuri mdgomareobebi (N 95.1)

WeSmariti gonaduri disgenezia (Q 99.1)terneris sindromi (Q96.-)

E28.8 sakvercxis funqciis sxva darRvevebisakvercxis hiperfunqcia, romelic sxvagvarad ar aris dazustebuli

E28.9 sakvercxis funqciis moSliloba, dauzustebeli

E saTesle jirkvlis disfunqcia

ar igulisxmeba: androgenTa mimarT rezistentobis sindromi (E 34.5)azoospermia an oligospermia, romelic sxvagvarad ar aris dazustebuli (E 23.0)goanadotropinis izolirebuli deficiti (E 23.0)klainefelteris sindromi (Q 98.0-Q 98.2, Q 98.4)saTesleebis postproceduruli hipofunqcia (E 89.5)testikuluri feminizacia (sindromi)(E 34.5)

E28

E29

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E29.0 saTesle jirkvlis hiperfunqciasaTeslis hormonebis hipersekrecia

E29.1 saTesle jirkvlis hipofunqciasaTeslis androgenebis defeqturi biosinTezi, romelic sxvagvarad ar

aris dazustebuli5-a -reduqtazis deficiti (mamakacur fsevdohermafroditizmTan erTad)testikuluri hipogonadizmi, romelic sxvagvarad ar aris dazustebuliTu wamlismieria da wamlis identifikacia gsurT, isargebled damatebiTi gare mizezTa

kodiT (Tavi XX)

E29.8 saTesle jirkvlis funqciis sxva moSlilobebiE29.9 saTeslis disfunqcia, dauzustebeli

sqesobrivi momwifebis darRvevebi, romelic ar aris Setanili sxva

klasifikaciebSi

EE30.0 sqesobrivi momwifebis Seferxeba

sqesobrivi simwifis konstituciuri Seferxeba

sqesobrivi ganviTarebis Seferxeba

E30.1 naadrevi sqesobrivi momwifebanaadrevi menstruaciaar igulisxmeba: olbrait (-makkunis)(-Sternbergis) sindromi (Q 78.1)

centraluri naadrevi sqesobrivi simwife (E 22.8)Tirkmelzeda jirkvlis Tandayolili hiperplazia (E 25.0)qalTa heteroseqsualuri naadrevi cru sqesobrivi simwife (E 25.-)mamakacTa izoseqsualuri naadrevi cru sqesobrivi simwife (E 25.-)

E30.8 sqesobrivi momwifebis sxva darRvevebisarZeve jirkvlis naadrevi momwifeba

E30.9 sqesobrivi momwifebis darRveva, dauzustebeli

poliglanduluri disfunqcia

ar igulisxmeba: ataqsia telangieqtazia (luis-baris) (G 11.3)miotonuri distrofia (Steniertis) (G 71.1)fsevdohipoparaTiroidizmi (E 20.1)

E31.0 autoimunuri poliglanduluri ukmarisobaSmidtis sindromi

E31.1 poliglanduluri hiperfunqciaar igulisxmeba:mravlobiTi endokrinuli adenomatozi (P 44.8)

E31.8 sxva saxis poliglanduluri disfunqciaE31.9 poliglanduluri disfunqcia, dauzustebeliE

Timusis avadmyofobebi

ar igulisxmeba: : : : : aplazia an hipoplazia imunodeficitTan erTad (D 82.1)miasTenia gravis (G 70.0)

E32.0 Timusis persistuli hiperplaziaTimusis hipertrofia

E32.1 Timusis abscesiE32.8 Timusis sxva avadmyofobebiE32.9 Timusis daavadeba, dauzustebeliE

E30

E31

E32

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avadmyofobaTa saerTaSoriso klasifikacia

sxva endokrinuli darRvevebi

ar igulisxmeba: fsevdohipoparaTiroidizmi (E 20.1)E34.0 karcinoiduli sindromi

SeniSvna: Tu gsurT karcinoidul simsivnesTan dakavSirebuli funqciuri aqtivobis

identifikacia, SegiZliaT gamoiyenoT damatebiTi kodi

E34.1 nawlavuri hormonebis sxva saxis hipersekreciaE34.2 hormonis eqtopiuri sekrecia, romelic ar aris Setanili sxva klasifikaciebSiE34.3 qondriskacoba, romelic ar aris Setanili sxva klasifikaciebSi

qondriskacoba:

. romelic sxvagvarad ar aris dazustebuli

. konstituciuri

. laronis-tipi

. fsiqosocialuriar igulisxmeba: progeria (E 34.8)

rasel-silveris sindromi (Q 87.1)moklekidurebiani aRnagoba imunodeficitTan erTad (D 82.2)qondriskacoba:

. aqondroplaziuri (Q 77.4)

. hipoqondroplaziuri (Q 77.4). specifikuri dismorfuli sindromebis dros - sindromTa kodi aRiniSneba anbanuriindeqsis mixedviT. alimenturi (E 45). hipofizuri (E 23.0)

. Tirkmlismieri (N 25.0)E34.4 konstituciuri simaRle

konstituciuri gigantizmi

E34.5 androgen-rezistentuli sindromimamakacTa fsevdohermafroditizmi androgenuli rezistentobiT

periferiuli hormonuli receptoris dazianebareifenSteinis sindromi

testikuluri feminizacia (sindromi)

E34.8 sxva dazustebuli endokrinuli moSlilobebijalRuzisebri sxeulis funqciis moSla

progeria

E34.9 endokrinuli moSliloba, dauzustebelimoSliloba:

. endokrinuli, romelic sxvagvarad ar aris dazustebuli

. hormonuli, romelic sxvagvarad ar aris dazustebuli

endokrinuli jirkvlebis dazianebebi im avadmyofobebis dros, romlebic

Setanilia sxva klasifikaciebSi

EE35.0* farisebri jirkvlis dazianebebi im avadmyofobTa dros, romlebic

Setanilia sxva klasifikaciebSifarisebri jirkvlis tuberkulozi (A 18.8+)

E35.1* Tirkmelzeda jirkvlis dazianebebi im avadmyofobaTa dros, romlebicSetanilia sxva klasifikaciebSituberkulozuri adisonis avadmyofoba (A 18.7+)vaterhauz-frideriksenis sindromi (meningokokuri) (A 39.1+)

E35.8* sxva endokrinul jirkvlebis dazianebani im avadmyofobTa dros, romlebicSetanilia sxva klasifikaciebSi

E34

E35*

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

sakvebis arasakmao raodenobiT miReba

(E40-E46)

SeniSvna:malnutriciis xarisxi Cveulebriv ganisazRvreba wonis mixedviT da gamoixateba SesabamisiSesaswavli mosaxleobis wonis saSualo sididis normidan gadaxris standartulimaCvenebliT. roca winaswar Catarebulia erTze meti gamokvleva, wonis matebis CamorCenabavSvebSi an bavSvebisa da mozrdilebis wonaSi dakleba, Cveulebriv, sakvebis arasakmarisadmiRebis maCvenebelia. Tu wonaze dakvirveba mxolod erTxel iqna nawarmoebi, diagnozisavaraudoa da ar iTvleba sabolood dadgenilad sxva klinikuri an laboratoriulimonacemebis gareSe. gamonaklis SemTxvevebSi, roca awonva ver xerxdeba, unda daveyrdnoTklinikur dakvirvebas. im SemTxvevebSi, Tu individuumis wonis maCvenebeli mocemulimosaxleobis wonis saSualo sidideze dabalia: mZime malnutricias varaudoben rocawonis normidan qvemoT gadaxra tolia an aRemateba 3 standartul maCvenebels.mosaxleobis wonis saSualo maCvenebelTan SedarebiT: zomier malnutricias varaudoben,roca wonis normidan qvemoT gadaxra aRemateba 2-s da naklebia 3 standartul maCvenebelze;msubuq malnutriciaze msjeloben, roca normidan qvemoT gadaxra aRemateba 1-s, magramnaklebia 2 standartul maCvenebelze.

ar igulisxmeba:nawlavuri malabsorbcia (K 90.-)alimenturi anemiebi (D 50-D 53)cila-energetikuli deficitis Sedegebi (E 64.0)sigamxdre (B 22.2)SimSili (starvacia)(T 73.0)

E kvaSiorkori

mZime malnutricia alimenturi SeSupebiT kanisa da Tmebis pigmentaciis moSlasTan erTad

ar igulisxmeba: marazmuli kvaSiorkori (E 42)E

alimenturi marazmi

mZime malnutricia marazmiT

ar igulisxmeba: marazmuli kvaSiorkori (E 42)E

marazmuli kvaSiorkori

mZime cila-energetikuli malnutricia (rogorc E 43). gardamavali forma

. kvaSiorkorisa da marazmis niSnebiT

E mZime cila-energetikuli deficiti

wonaSi didi raodenobiT dakleba [ganleva] bavSvebsa da mozrdilebSi, an wonaSi matebisCamorCena bavSvebSi, romlis Sedegad miRebuli wonis maCvenebeli sul mcire, 3 erTeuliTCamorCena Sesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi daklebaaRiniSneba sxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTidakvirveba, mZime ganlevas varaudoben maSin, roca miRebuli wonis maCvenebeli 3 da metierTeuliT CamorCeba Sesabamisi mosaxleobis wonis saSualo sidides.

starvaciuli SeSupeba

Ezomieri da msubuqi xarisxis cila-energetikuli deficiti

EE44.0 zomieri cila-energetikuli malnutricia

wonis kargva bavSvebsa da mozrdilebSi; an wonaSi matebis CamorCena bavSvebSi, romlisSedegad miRebuli wonis maCvenebeli 2 an meti, magram 3-ze naklebi erTeuliT CamorCenaSesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi dakleba aRiniSnebasxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTi dakvirveba,zomier cila-energetikul malnutricias varaudoben maSin, roca miRebuli wonis

E40

E41

E42

E43

E44

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avadmyofobaTa saerTaSoriso klasifikacia

maCvenebeli 2 an meti, magram 3-ze naklebi erTeuliT CamorCeba Sesabamisi mosaxleobis

wonis saSualo sidides.

E44.1 msubuqi cila-energetikuli malnutriciawonis kargva bavSvebsa da mozrdilebSi an wonaSi matebis CamorCena bavSvebSi, romlisSedegad miRebuli wonis maCvenebeli 1 an meti, magram 2-ze naklebi erTeuliT CamorCebaSesabamisi mosaxleobis wonis saSualo maCvenebels (an wonaSi msgavsi dakleba aRiniSnebasxva statistikuri gamokvlevebis drosac). Tu Catarebulia mxolod erTi dakvirveba,msubuq cila-energetikul malnutricias varaudoben maSin, roca miRebuli wonismaCvenebeli 1 an meti, magram 2-ze naklebi erTeuliT CamorCeba Sesabamisi mosaxleobis

wonis saSualo sidides.

zrda-ganviTarebaSi CamorCena, gamowveuli cila-energetikuli deficitiT

alimenturi:

. qondriskacoba

. zrdis SeCerebafizikuri ganviTarebis Seferxeba, gapirobebuli sakvebis arasakmao raodenobis miRebiT

(malnutriciiT)

E dauzustebeli cila-energetikuli deficiti

SimSiloba, romelic sxvagvarad ar aris dazustebuli

cila-energetikuli disbalansi, romelic sxvagvarad ar aris dazustebuli

kvebiTi deficitis sxva saxeebi

(E50-E64)ar igulisxmeba: alimenturi anemiebi (D 50-D 53)E

A vitaminis deficitiar igulisxmeba: vitamin A deficitis Sedegebi (E 64.1)

E50.0 vitamin A deficiti koniunqtivis qseroziT (simSraliT)E50.1 vitamin A deficiti bitotis laqiTa da koniunqtivis qseroziT (simSraliT)

bitotis laqa mcirewlovan bavSvebSi

E50.2 vitamin A deficiti rqovanas qseroziT (simSraliT)E50.3 vitamin A deficiti rqovanas dawylulebiTa da qseroziT (simSraliT)E50.4 vitamin A deficiti keratomalaciiTE50.5 vitamin A deficiti Ramis sibrmaviTE50.6 vitamin A deficiti rqovanas qserofTalmuri nawiburebiTE50.7 vitamin A deficitis sxva gamovlinebebiT Tvalis mxriv

qserofTalmia, romelic sxvagvarad ar aris dazustebuli

E50.8 vitamin A deficitis sxva gamovlinebebifolikuluri keratozi

qseroderma

E50.9 vitamin A deficiti, dauzustebulihipovitaminozi A, romelic sxvagvarad ar aris dazustebuli

Tiaminis deficiti

ar igulisxmeba: Tiaminis deficitis Sedegebi (E 64.8)E51.1 beri-beri

beri-beri:

E45

E46

E50

E51

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

. mSrali

. sveli + (I 98.8*)

E51.2 vernikes encefalopaTiaE51.8 Tiaminis deficitis sxva gamovlinebebiE51.9 Tiaminis deficiti, dauzustebeliE

nikotinmJavas deficiti [pelagra]

deficiti:. niacin (- triftofanis). nikotinamidispelagra (alkoholuri)ar igulisxmeba: niacinis deficitis Sedegebi (E 64.8)

E

B jgufis sxva vitaminebis deficitiar igulisxmeba: vitamin B deficitis Sedegebi (E 64.8)

vitamin B12 deficituri anemia (D 51.-)E53.0 riboflavinis deficiti

ariboflavinozi

E53.1 piridoqsinis deficitivitimin B6

deficiti

ar igulisxmeba: piridoqsin damokidebuli sideroblasturi anemia (D 64.3)E53.8 B B jgufis vitiminebis sxva dazustebuli saxis deficiti

deficiti:

. biotinis

. ciankobalaminis

. folatis

. foliumis mJavis

. panTotenis mJavis

. vitamin B12-isE53.9 vitamin B deficiti, dauzustebeli

askorbinis mJavis deficiti

vitamin C deficiti

skorbuti [suravandi]ar igulisxmeba: skorbutuli anemia (D 53.2)

vitamin C deficitis Sedegebi (E 64.2)E

D vitaminis deficitiar igulisxmeba: mozrdilTa osteomalacia (M 83.-)osteoporozi (M 80-M 81)raqitis Sedegebi (E 64.3)

E55.0 raqiti, aqtiuriosteomalacia:

. bavSvTa

. mozardTaar igulisxmeba: raqiti:

. celiakuri (K 90.0)

. kronis (K 50.-)

. araaqtiuri (E 64.3)

. Tirkmlismieri (N 25.0)

. vitamin-D-rezistentuli (E 83.3)

E55

E54

E52

E53

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avadmyofobaTa saerTaSoriso klasifikacia

E55.9 vitamin D-s deficiti, dauzustebeliavitaminozi D

Esxva vitaminebis deficiti

ar igulisxmeba:sxva vitaminebis deficitis Sedegebi (E 64.8)E56.0 vitamin E-s deficitiE56.1 vitamin K-s deficiti

ar igulisxmeba:vitamin K-s deficitiT gamowveuli koagulaciuri faqtoris deficiti (D 68.4)axalSobilTa vitamin K-s deficiti (P 53)

E56.8 sxva vitaminebis deficitiE56.9 vitaminis deficiti, dauzustebeli

E sakvebSi kalciumis deficiti

ar igulisxmeba: kalciumis cvlis darRvevebi (E 83.5)kalciumis deficitis Sedegebi (E 64.8)

sakvebSi seleniumis deficiti

keSanis avadmyofoba

ar igulisxmeba: seleniumis deficitis Sedegebi (E 64.8)E

sakvebSi TuTiis deficiti

E

sxva sakvebi elementebis deficiti

Tu wamlismieria da wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare mizezebiskodi (Tavi XX)ar igulisxmeba: mineraluri cvlis darRvevebi (E 83.-) iodis deficitTan dakavSirebuli

farisebri jirkvlis avadmyofobebi (E00-E02) malnutriciis da sxva kvebiTi deficitis Sedegebi (E 64.-)

E61.0 spilenZis deficitiE61.1 rkinis deficiti

ar igulisxmeba: rkina-deficituri anemia (D 50.-)E61.2 magniumis deficitiE61.3 manganumis deficitiE61.4 qromis deficitiE61.5 molibdenis deficitiE61.6 vanadiumis deficitiE61.7 ramdenime sakvebi elementis erTdrouli deficitiE61.8 sxva dazustebuli sakvebi elementis deficitiE61.9 sakvebi elementis deficiti, dauzustebeli

sxva kvebiTi deficiti

ar igulisxmeba: dehidracia (E 86)zrdaSi CamorCena (R 62.8)axalSobilTa kvebis problemebi (P 92.-)malnutriciis da sxva kvebiTi deficitis Sedegebi (E64.-)

E63.0 esenciuri cximovani mJavebis deficitiE63.1 miRebuli sakvebis Semadgeneli nawilebis balansis darRvevaE63.8 sxva dazustebuli kvebiTi deficitebi

E56

E58

E59

E60

E61

E63

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E63.9 sakvebis deficiti, dauzustebelialimenturi kardiomiopaTia, romelic sxvagvarad ar aris dazustebuli (I 43.2*)

Ekvebis deficitisa da sxva sakvebi elementebis deficitis Sedegebi

EE64.0 cila-energetikuli deficitis Sedegebi

ar igulisxmeba:zrda-ganviTarebis Seneleba, gamowveuli cila-energetikuli deficitiT (E45)E64.1 vitamin A deficitis SedegebiE64.2 vitimin C deficitis SedegebiE64.3 raqitis SedegebiE64.8 sakvebis naklebobis sxva SedegebiE64.9 sakvebis dauzustebeli deficitis Sedegebi

simsuqne da Warbi kvebis saxeebi

(E65-E68)E

adgilobrivi simsuqne

cximovani baliSi

E simsuqne

ar igulisxmeba: adipozo-genitaluri distrofia (E 23.6)lipomatozi:. romelic sxvagvarad ar aris dazustebuli (E 88.2). mtkivneuli (dolorosa) [derkumis] (E 88.2)prader-vilis sindromi (Q 87.1)

E66.0 Warbi kaloriebis Sedegad ganviTarebuli simsuqneE66.1 wamliT-gamowveuli simsuqne

Tu wamlis identifikacia gsurT, gamoiyeneT damatebiTi gare mizezebis kodi (Tavi XX)

E66.2 ukiduresi simsuqne alveoluri hipoventilaciiTpikvikis sindromi

E66.8 sxva saxis simsuqneavadmyofuri simsuqne

E66.9 simsuqne, dauzustebelimartivi simsuqne, romelic sxvagvarad ar aris dazustebuli

E

Warbi kvebis sxva saxeebi

ar igulisxmeba:hiperalimentacia, romelic sxvagvarad ar aris dazustebuli (R 63.2)hiperalimentaciis Sedegebi (E 68)

E67.0 hipervitaminozi AE67.1 hiperkarotinemiaE67.2 megavitamin-B6

sindromiE67.3 hipervitaminozi DE67.8 sxva dazustebuli hiperalimentaciebiE

hiperalimentaciis Sedegebi

E64

E65

E66

E67

E68

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avadmyofobaTa saerTaSoriso klasifikacia

metaboluri darRvevebi

(E70-E90)

ar igulisxmeba: androgen-rezistentuli sindromi (E 34.5)Tirkmelzeda jirkvlis Tandayolili hiperplazia (E 25.0)elers-danlosis sindromi (Q 79.6)fermentuli moSlilobebiT gapirobebuli hemolizuri anemiebi (D 55.-)marfanis sindromi (Q 87.4)5-a- reduqtazis deficiti (E 29.1)

aromatuli aminomJavebis metabolizmis darRvevebi

EE70.0 klasikuri fenilketonuriaE70.1 sxva hiperfenilalaninemiebiE70.2 Tirozinis metabolizmis darRvevebi

alkaptonuria

hiperTirozinemiaoqronoziTirozinemia

Tirozinozi

E70.3 albinizmialbinizmi:

. okuluri

. okulokutaneuri (Tval-kanis)sindromi:. Cediak (-Steinbrinq)-higaSis. krosis

. helmanski-pudlekis

E70.8 aromatuli aminomJavebis metabolizmis sxva darRvevebidarRveva:

. histidinis metabolizmis

. triftofanis metabolizmis

E70.9 aromatuli aminomJavis metabolizmis darRveva, dauzustebeli

ganStoebuljaWviani aminomJavebisa da cximovani mJavebis metabolizmis

darRvevebi

EE71.0 nekerCxlis sirofis msgavsi Sardis avadmyofobaE71.1 ganStoebuljaWviani aminomJavebis metabolizmis sxva darRvevebi

hiperleicin-izoleicinemia

hipervalinemiaizovalerianis acidemiameTilmalonis acidemia

propionis acidemia

E71.2 ganStoebuljaWviani aminomJavis metabolizmis darRveva, dauzustebeliE71.3 cximovani mJavebis metabolizmis darRvevebi

adrenoleikodistrofia [adison-Silderis]

kunTovani karnitinpalmitiltransferazis deficitiar igulisxmeba: revsamis avadmyofoba (G 60.1)

Silderis avadmyofoba (G 37.0)cilvegeris sindromi (Q 87.8)

E70

E71

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

aminomJavebis metabolizmis sxva darRvevebi

ar igulisxmeba:normidan gadaxrili monacemebi avadmyofobis gamovlinebis gareSe (R70-R89)

darRvevebi:. aromatuli aminomJavebis metabolizmis (E 70.-)

. . ganStoebuljaWviani aminomJavebis metabolizmis (E71.0-E71.2). cximovani mJavebis metabolizmis (E 71.3). purinisa da pirimidinis metabolizmis (E79.-)nikrisi (M 10.-)

E72.0 aminomJavebis transportis darRvevebicistinozi

cistinuriafankoni (-de toni) (-debres) sindromihartnafis avadmyofobaloves sindromi

ar igulisxmeba: triftofanis metabolizmis darRvevebi (E 70.8)E72.1 gogirdSemcveli aminomJavebis metabolizmis darRvevebi

cistaTioninuria

homocistinuriameTioninemiasulfitoqsidazis deficiti

ar igulisxmeba: transkobalamin II deficiti (D 51.2)E72.2 Sardovanas ciklis metabolizmis darRvevebi

argininemia

argininosukcinuri aciduriacitrulinemiahiperamonemia

ar igulisxmeba:ornitinis metabolizmis darRvevebi (E 72.4)E72.3 lizinisa da hidroqsilizinis metabolizmis darRvevebi

glutaris aciduria

hidroqsilizinemia

hiperlizinemia

E72.4 ornitinis metabolizmis darRvevebiirnitinemia (tipi I, II)

E72.5 glicinis metabolizmis darRvevebihiperhidroqsiprolinemia

hiperprolinemia (tipi I, II)ara-ketonuri hiperglicinemia

sarkozinemia

E72.8 aminomJavebis metabolizmis sxva dadgenili darRvevebidarRvevebSi:

. bB-aminomJavis metabolizmis

. g-glutamilis ciklis

E72.9 aminomJavebis metabolizmis moSla, dauzustebeli

E laqtozis autanloba

E73.0 laqtozis Tandayolili deficitiE73.1 laqtozis meoradi deficitiE73.8 laqtozis sxva saxis autanlobaE73.9 laqtozis dauzustebeli autanloba

E72

E73

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avadmyofobaTa saerTaSoriso klasifikacia

E naxSirwylebis metabolizmis sxva darRvevebi

ar igulisxmeba: glukagonis gazrdili sekrecia (E 16.3)Saqriani diabeti (E 10-E 14)hipoglikemia, romelic sxvagvarad ar aris dazustebuli (E 16.2)mukopolisaqaridozi (E 76.0-E 76.3)

E74.0 glikogenis dagrovebis avadmyofobagulis glikogenozi

avadmyofoba:. andersenis. koris. forbesis. hersis. makardlis. pompes. tauris. fon girkes

. RviZlis fosforilazis deficiti

E74.1 fruqtozis metabolizmis darRvevebiesenciuri fruqtozuria

fruqtozo-1,6-difosfatazis deficiti

fruqtozis memkvidruli autanloba

E74.2 galaqtozis metabolizmis darRvevebigalaqtokinazis deficiti

galaqtozemia

E74.3 nawlavebSi naxSirwylebis Sewovis sxva darRvevebSiglukoza-galaqtozis malabsorbcia

saqarozis ukmarisoba

ar igulisxmeba: laqtozis autanloba (E 73.-)E74.4 piruvatis metabolizmis da glukoneogenezis darRvevebi

deficiti:

. fosfoenolpiruvatkarboqsikinazis

. piruvatis

. karboqsilazis

. dehidrogenazis

ar igulisxmeba: anemiasTan erTad (D 55-)E74.5 naxSirwylebis metabolizmis sxva specifiuri darRvevebi

esenciuri pentozuria

oqsalozioqsaluria

Tirkmlismieri glukozuria

E74.9 naxSirwylebis metabolizmis darRveva, dauzustebeli

sfingolipidebis metabolizmis darRvevebi da lipidebis dagrovebis sxva

darRvevebi

ar igulisxmeba: mukolipidozi, tipi III (E 77.0-E 77.1)revsamis avadmyofoba (E 60.1)

E75.0 GM2 gangliozidoziavadmyofoba:

. sandhofis

. Tei-saqsisGM2 ganliozidozi:

E71E74

E75

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

.Nromelic sxvagvarad ar aris dazustebuli

. mozrdilTa

. mozardTa

E75.1 sxva gangliozidozebigangliozidozi:

. romelic sxvagvarad ar aris dazustebuli

. GM1

. GM3

mukolipidozi IV

E75.2 sxva sfingolipidozebiavadmyofoba:

. fabris (-andersonis)

. goSes

. krabes

. niman-pikisfarberis sindromimetaqromuli leikodistrofiasulfatazis deficiti

ar igulisxmeba: adrenoleikodistrofia (adison-Silderis) (E 71.3)E75.3 sfingolipidozi, dauzustebeliE75.4 neironuli ceroiduli lipofuscinozi

avadmyofoba:

. batenis

. bilSovski-ianskis

. kafis

. Spilmeier-vogtis

E75.5 sxva lipidebis dagrovebiT mimdinare avadmyofobebicerebrotendinuri qolesterozi (van bogart-Serer-ebSteinis)

volmanis avadmyofoba

E75.6 lipidebis dagrovebis darRvevebi, dauzustebeli

glikozaminoglikanebis darRvevebi, dauzustebeli

E

E76.0 mukopolisaqaridozi, tipi Isindromi:

. harleris

. harker-Seies

. Seies

E76.1 mukopolisaqaridozi, tipi IIhanteris sindromi

E76.2 sxva mukopolisaqaridozebib-glukuronidazis deficiti

mukopolisaqaridozi, tipi III,IV,VI,VIIsindromi:. maroto-lamis (msubuqi) (mZime). morkuios (-msgavsi) (klasikuri)

. sanfilipos (tipi B)(tipi C)(tipi D)E76.3 mukopolisaqaridozi, dauzustebeliE76.8 glikozaminoglikanebis metabolizmis sxva darRvevebiE76.9 glikozaminoglikanis metabolizmis darRveva, dauzustebeliE

E76

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avadmyofobaTa saerTaSoriso klasifikacia

glikoproteinebis metabolizmis darRvevebi

E77.0 lizosomuri fermentebis posttranslaciuri modifikaciis defeqtebimukolipidozi II (I-ujredis avadmyofoba)

mukolipidozis III (fsevdo-harleris polidistrofia)

E77.1 glikoproteinis daSlis defeqtebiaspartilglukozaminuria

fukozidozimanozidozi

sialidozi (mukolipidozi I)

E77.8 glikoproteinebis metabolizmis sxva darRvevebiE77.9 glikoproteinis metabolizmis darRveva, dauzustebeli

E lipoproteinebis metabolizmis darRvevebi da sxva lipidemiebi

ar igulisxmeba: sfingolipidozi (E 75.0-E 75.3)E78.0 WeSmariti hiperqolesterinemia

ojaxuri hiperqolesterinemia

fredriqsonis hiperlipoproteinemia, tipi IIaühiper -b-lipoproteinemiahiperlipidemia, jgufi Adabali simkvrivis lipoproteinuli tipis (LDL) hiperlipoproteinemia

E78.1 WeSmariti hipergliceridemiaendogenuri hipergliceridemia

fredriqsonis hiperlipoproteinemia, tipi IVhipirlipidemia, jgufi Bhiperpre -b-lipoproteinemiaZalian dabali simkvrivis lipoproteinuli tipis (VLDL)hiperlipoproteinemia

E78.2 Sereuli hiperlipidemiafarTe anu flotirebuli b- lipoproteinemia

fredriqsonis hiperlipoproteinemia, tipi IIbü an IIIhiper-b-lipoproteinemia pre-b-lipoproteinemiiThiperqolesterinemia endogenuri hipergliceridemiiThiperlipidemia, jgufi Ctubero-eruptiuli tipis qsanTomatuberozuli qsanToma (Xanthoma tuberosum)ar igulisxmeba: cerebrotendinuri qolesterozi (van bogart-Serer-epSteinis) (E 75.5)

E78.3 hiperqilomikronemiafredriqsonis hiperlipoproteinemia, tipi I an V

hiperlipidemia, jgufi DSereuli hipergliceridemia

E78.4 sxva hiperlipidemiebiojaxuri kombinirebuli hiperlipidemia

E78.5 hiperlipidemia, dauzustebeliE78.6 lipoproteinTa deficiti

a-b-lipoproteinemia

maRali-simkvrivis lipoproteinTa deficitihipo-a-lipoproteinemiahipo-b-lipoproteinemia (ojaxuri)

lecitinqolesterolaciltransferazis deficiti

teinjeris avadmyofoba

E77

E78

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

E78.8 lipoproteinebis metabolizmis sxva darRvevebiE78.9 lipoproteinebis metabolizmis moSla, dauzustebeli

E purinebis da pirimidinebis metabolizmis darRvevebi

ar igulisxmeba: Tirkmlis kenWi (N 20,0)kombinirebuli imunodeficituri darRvevebi (D 81.-)nikrisi (podagra) ( M 10.-)orotaciduriuli anemia (D 53.0)pigmenturi qseroderma (Q 82.1)

E79.0 hiperurikemia anTebiTi arTritisa da podagruli avadmyofobis niSnebisgareSeasimptomuri hiperurikemia

E79.1 leS-nihenis sindromiE79.8 purinisa da pirimidinis metabolizmis sxva darRvevebi

memkvidruli qsanTinuria

Eporfirinebisa da bilirubinis metabolizmis darRvevebi

igulisxmeba:katalazis da peroqsidazis defeqtebi

E80.0 memkvidruli eriTropoezuri porfiriaTandayolili eriTropoezuri porfiria

eriTropoezuri protoporfiria

E80.1 kanis gviani porfiriaE80.2 sxva saxis porfiria

memkvidruli koproporfiria

porfiria:.Nromelic sxvagvarad ar aris dazustebuli. mwvave xangamoSvebiTi (RviZlis)

Tu mizezis identifikacia gsurT, isargebleT damatebiT gare mizezTa kodiT (Tavi XX)

E80.3 katalazis da peroqsidazis defeqtebiakatalazia (takapara)

E80.4 jilbertis sindromiE80.5 krigler-najaris sindromiE80.6 bilirubinis metabolizmis sxva darRvevebi

dubin-jonsonis sindromi

rotorsis sindromi

E80 .7 bilirubinis metabolizmis moSla, dauzustebeliE

mineraluri cvlis darRvevebi

ar igulisxmeba: sakvebi mineralebis deficiti (E 58-E 61)farisebralo jirkvlis avadmyofobebi (E 20-E 21)vitamin D-s deficiti (E 55.-)

E83.0 spilenZis metabolizmis darRvevebimenkes (xveuli Tmis) (foladisebri Tmis) avadmyofoba

vilsonis avadmyofoba

E83.1 rkinis metabolizmis darRvevebihemoqromatozi

ar igulisxmeba: .anemia:. rkinadeficituri (D 50.-). sideroblasturi (D 64.0-D 64.3)

E79

E83

E80

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avadmyofobaTa saerTaSoriso klasifikacia

E83.2 TuTiis metabolizmis darRvevebieteropaTiuli akrodermatiti

E83.3 fosforis metabolizmis darRvevebimJave fosfatazis deficiti

ojaxuri hipofosfatemiahipofosfataziavitamin - D -rezistenuli:. osteomalacia. raqiti

ar igulisxmeba: mozrdilTa osteomalacia (M 83.-)osteoporozi (M 80.-M 81)

E83.4 magniumis metabolizmis darRvevebihipermagniemia

hipomagniemia

E83.5 kalciumis metabolizmis darRvevebiojaxuri hipokalciuriuli piperkalciemia

idiopaTiuri piperkalcinozi

ar igulisxmeba: qondrokalcinozi (M 11.1-M 11.2)hiperparaTiroidizmi (E 21.0 -E 21.3)

E83.8 mineraluri metabolizmis sxva darRvevebiE83.9 mineralTa metabolizmis darRvevebi, dauzustebeliE

cisturi fibrozi

igulisxmeba: mukoviscidozi

E84.0 cisturi fibrozi pulmonuri gamovlinebebiTE84.1 cisturi fibrozi nawlavuri gamovlinebebiTE84.8 cisturi fibrozi sxva gamovlinebebiT

cisturi fibrozi kombinirebuli gamovlinebebiT

E84.9 cisturi fibrozi dauzustebeli

amiloidozi

ar igulisxmeba: alchaimeris avadmyofoba (G 30.-)E85.0 araneiropaTiuli memkvidruli ojaxuri amiloidozi

xmelTaSuazRvispiruli ojaxuri cxeleba

memkvidruli amiloiduri nefropaTia

E85.1 neiropaTiuli memkvidruli ojaxuri amiloidoziamiloiduri polinevropaTia (portugaliuri)

E85.2 memkvidruli ojaxuri amiloidozi dauzustebeliE85.3 meoradi sistemuri amiloidozi

hemodializTan dakavSirebuli amiloidozi

E85.4 gansazRvrul organoSi ganviTarebuli amiloidozilokalizebuli amiloidozi

E85.8 sxva amiloidozebiE85.9 amiloidozi daudgeneli

E moculobis Semcireba

dehidracia

sisxlis plazmis moculobis an ujredSorisi siTxis moculobis Semcirebahipovolemia

E86

D84

E85

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endokrinuli sistemis, kvebisa da nivTierebaTa cvlis darRveviT gamowveuli avadmyofobani

ar igulisxmeba: axalSobilTa dehidracia (P 74.1)hipovolemiuri Soki:. romelic sxvagvard ar aris dazustebuli (R 57-1). postoperaciuli (T 81.1). travmuli (T 79.4)

siTxeebis, eleqtrolitebis da mJava-tutovani wonasworobis sxva

darRvevebi

E87.0 hiperosmolaroba da hipernatriemiaNa-is siWarbe

Na-iT gadatvirTva

E87.1 hipoosmolaroba da hiponatriemiaNa-is deficitiar igulisxmeba: antidiurezuli hormonis Seusabamo sekreciis sindromi (E 22.2)

E87.2 acidoziacidozi:.Nromelic sxvagvarad ra aris dazustebuli. rZis mJavis. metaboluri. respiraciuli

ar igulisxmeba: diabeturi acidozi (E 10-E 14 saerTo meoTxe rigiT.1)

E87.3 alkalozialkalozi.Nromelic sxvagvarad ar aris dazustebuli. metaboluri

. respiraciuli

E87.4 mJava-tutovani wonasworobis Sereuli darRvevebiE87.5 hiperkaliemia

K-is siWarbe

K-iT gadatvirTva

E87.6 hipokalemiaK-is deficiti

E87 .7 qsovilovani siTxis siWarbear igulisxmeba: SeSupeba (R 60.-)

E87.8 siTxisa da eleqtrolitTa balansis sxva darRvevebi romlebic ar arisSetanili sxva klasifikaciebSieleqtrolituri disbalansi, romelic sxvagvarad ar aris dazustebuliNOhiperqloremia

hipoqloremia

sxva metaboluri darRvevebi

ar igulisxmeba: histiocitozi X (qronikuli) (D 76.0)Tu wamlismieria da wamlis identifikacia gsurT, isargebleT damatebiT

gare mizezTa kodiT (Tavi XX)

E88.0 sisxlis plazmis cilebis metabolizmis, darRvevebi, romelic ar arisSetanili sxva klasifikaciebSia-1-antitrifsinis deficitibis-albuminemiaar igulisxmeba: lipoproteinebis metabolizmis moSla (E 78.-)

E87

E88

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210

avadmyofobaTa saerTaSoriso klasifikacia

monoklonuri gamapaTia (D 47.2)poliklonuri hipergamaglobulinemia (D 89.0)valdenStromis makroglobulinemia (C 88.0)

E88.1 lipodistrofia, romelic ar aris Setanili sxva klasifikaciebSilipodistrofia, romelic sxvagvarad ar aris dazustebuli

ar igulisxmeba: uiplis avadmyofoba (K 90.8)E88.2 lipomatozi, romelic ar aris Setanili sxva klasifikaciebSi

lipomatozi.Nromelic sxvagvarad ar aris dazustebuli

. mtkivneuli (dolorosa) (derkumis)

E88.8 sxva dadgenili metaboluri darRvevebibensaudis adenolipomatozi - lavnua

trimeTilaminuria

E88.9 metaboluri darRveva daudgeneli

procedurebis Semdgomi endokrinuli da metaboluri darRvevbi, romlebic

ar aris Setanili sxva klasifikaciebSi

E89.0 postproceduruli hipoTiroidizmipostiradiaciuli hipoTiroidizmi

postoperaciuli hipoTiroidizmi

E89.1 postproceduruli hipoinsulinemiapankreasis amokveTis Semdgomi hiperglikemia

E89.2 postproceduruli hipoparaTiroidizmifarisebraxlo jirkvlis ararsebobiT gamowveuli tetania

E89.3 postproceduruli hipopituitarizmipostiradiaciuli hipopituitarizmi

E89.4 sakvercxis postproceduruli ukmarisobaE89.5 saTesle jirkvlebis postproceduruli hipofunqciaE89.6 Tirkmelzeda jirkvlis (tvinovani Sris) postprceduruli hipofunqciaE89.8 sxva postproceduruli endokrinuli da metaboluri darRvevebiE89.9 postproceduruli da metaboluri darRvevebi, daudgeneli

alimenturi da metaboluri darRvevebi im avadmyofobebis dros, romlebic

Setanilia sxva klasifikaciebSi

E90*

E89