Double inlet Left Ventricle

Apical four chamber view showing double inlet left ventricle. Note the presence of two atrioventricular valves connecting to a single morphology left ventricle.

RA

RV

LA

LVMLV

LARA LA

Fig 53

Tricuspid atresia

LV

RV

RA

LA

Apical four chamber view from a patient with an absent right atrioventricular connection (tricuspid atresia). The position of the tricuspid valve is replaced by strand of tissue (arrow).The right ventricular cavity is very small. A perimembranous VSD is also present.

vsd

Fig 54

CLASSICAL GLENN

SVC

RA

IVC

RPA LPA

BIDIRECTIONAL GLENN

SVC

PA

RA

IVC

FONTAN

PA

RA

TOTAL CAVOPULMONARY CONNECTION

PA

SVC

IVC

RA

Fig 55

Tricuspid atresia

Apical four chamber view of a univentricular atrioventricular connection with atresia of theright sided atriovenricular valve (tricuspid atresia).The patient had a Fontan type repair (right atrium to pulmonary artery connection). The valve between the IVC and right atrium can just be seen in the right atrium (arrow).

RA

MLV

LA

Fig 56

TCPC

Apical four chamber view of a patient with auniventricular atriovenricular connectionand a common atrium, post TCPC. Note the TCPC pathway (arrow) at the back of the atrium.

Common atrium

V

Fig 57

Tricuspid atresia post Fontan operation

Apical view of a univentricular atrioventricular connection resulting from atresia of the right-sided atrioventricular valve (tricuspid atresia). The patient had a Fontan type operation. Note that the right atrium is severely dilated with thrombus inside.

RA

LV

LA

Fig 58

Fontan: The giant RA and large clot

TOE image taken from a patient with a double inlet left ventricle post Fontan (atria-pulmonaryconnection) repair. Note the severely dilated right atrium with giant thrombus and spontaneous contrast inside the atrial chamber (arrow).

RA RA

Fig 59