classification & management of legg calve perthes disease
TRANSCRIPT
RADIOGRAPHY
MAGNETIC RESONANCE IMAGING
BONE SCINTIGRAPHY
ULTRASONOGRAPHY
ARTHOGRAPHY
COMPUTED TOMOGRAPHY
Plain X ray of PELVIS WITH BOTH HIP JTS AP view Lowenstein’s frog-leg lateral view Abduction – Adduction views
Knee joints – AP / Lat Wrist joints – AP / Lat
Waldenstrom’s classification – four stages INITIAL STAGE FRAGMENTATION STAGE REOSSIFICATION (HEALING) STAGE RESIDUAL STAGE
Smaller osiffic nucleus
Lateralization of femoral head in the acetabulum
Widening of medial jt space
Waldenstrom / caffeys sign Vaccum phenomenon
Radio-dense femoral head
Cyst & leucency in metaphysis
END OF STAGE: appearance of lucencies in nucleus
6m( up to14m)
Lucent areas appear in the ossific nucleus of femoral head
Demarcation of femoral segments (pillars) – often central dense
Milder form – only ant segement seen on frog-leg lateral
More severe – no demarcation of pillars
END OF STAGE – appearance of new bone in subchondral area
8m(2 – 35m)
STARTS WITH - appearance of new bone in subchondral area
first in center of head – then expands medially and laterally
Anterior segment – last to reossify Process- lucent/necrotic areas of
fragmentation stage replaced by WOVEN BONE which then ossifies , remodels in to TRABECULAR BONE
mild gradual flatenning – children < 5
yrs whose femoral head is totally involved
most improve 51m(2-122m)
femoral head is fully reossified head remodels so does the
acetabulum Head – normal / extremely flat /
aspherical Physis is inlvolved – overgrowth of
greater trochanter
Gill(1940) – metaphyseal necrosis & lucencies (“holes of decalcification”)
Ponseti – cystic changes in neck Prognostic
value – poor outcome
Sagging rope sign
radiodense line in prox femoral metaphysis
Metaphyseal response to physeal damage
Premature physeal closure
With central arrests: Round head Short neck Troch overgrowth
With lateral arrest: Femoral head tilted Laterally Elongation of medial neck Overgrowth of troch
Morphological changes in acetabulum in perthes described by BENJAMIN JOSEPH (JBJS 1989)
Osteoporosis of acetabular roof Irregularity of contour Premature fusion of triradiate cartilage
( bicomparmentalisation) Hypertrophy of articular cartilage &
changes in dimension
BICOMPARTMENTALIZATION – When femoral head protrudes from
acetabulum - medial wall may form And look like a second compartment for the
head
Bicompartmental acetabulum in perthes disease (JBJS 87-B aug 2005)
On plain xray - bicompartmental acetabulum appears to be composed of 2 arc partly overlapping each other – interpreted as the subluxated femoral head articulating only with the lateral half of the acetabulum moulding it into 2 compartments
Used for early diagnosis of LCP disease
Detects – Configuration of femoral head &
acetabulum Congruity of articular surface Femoral head containment Joint effusion
Synovial hypertrophy Epiphyseal involvement True extent of femoral head necrosis
helps in diagnosis of early
stages visualization of early
reperfusion
Transphyseal reperfusion, occurring by neovascularization through the physis, is known to be a strong predictor of growth deformity.
Effective tool for diagnosis of pre-radiological early stages
Revascularization patterns
Findings of Configuration of head Widening of joint space due to thickend
cartilage Lateral shifting of head Containment of head within acetabulum
Major Advantage – assessment of congruity of joint in different range of movement
Currently, mainly used in early diagnosis of HINGED ABDUCTION
In early stages - Joint effusion
In later stages – assess shape of cartilagenous femoral head
provides acurate 3 D images of shape of femoral head & acetabulum
1. LEGG2. WALDENSTROM3. GOFF4. SALTER THOMPSON 5. CATERALL 6. HERRING’S LATERAL PILLAR7. MOSE8. STULBERG
LEGG – two types of head A “cap” & a “mushroom”(more severe)
WALDENSTROM – classified head 3 categories Type 1 & 2 with good results Type 3 – altered shape leading to restriction of
ROM to only flexion & extension (conical)
GOFF – 3 types of head Spherical, cap, irregular
Extent of subchondral # in both AP & lowenstein frog leg lateral xrays
reliable indicator in the group with fractures
extent of the fracture (line) is less than 50% of the superior dome of the femoral head› good results can be expected.
Extent of the fracture is more than 50% of the dome, › fair or poor results can
be expected
In 1971 used radiological findings of
epiphyseal involvement to identify 4 groups
anterior femoral head involvement
no evidence of sequestrum, subchondral fracture line, or metaphyseal abnormalities
anterolateral involvement
Central sequestrum
Well demarcated
metaphyseal lesions
Subchondral fracture line – Ant ½
lateral column is intact.
large sequestrum - 3/4th of head.
Junction is sclerotic.
Diffuse Metaphyseal lesions , anterolaterally
Subchondral fracture line - post 1/2
The lateral column is involved.
Entire head
Diffuse or central metaphyseal lesions
posterior
remodeling of the epiphysis
1. Gage sign : Described by COURTNEY GAGE(1933) small osteoporotic segment which forms a radiolucent V-shaped defect on lateral epiphysis & adjacent metaphysis on AP xray .
2. Speckled calcification lateral to epiphysis
3. Lateral subluxation of femoral head4. Horizontally oriented physis5. Diffuse metaphyseal reaction
(metaphyseal cysts)
Based on radiographic changes in lateral portion of femoral head during fragmentation stage on AP view
LATERAL PILLAR - lateral 15-30% of epiphysis on AP xray
Group A – no involvement
Group B – at least 50 % of height maintained
Group C – less than 50% of height maintained
Advantage
Easy application in active disease
High correlation bet lat pillar height and amount of head flattening at skeletal maturity
Based on fitting of contour of healed femoral head to template of concentric circles in both AP & Frog leg lateral views
Good - < 1 mm Fair - < 2 mm Poor - > 2 mm
described in 1981 Alike MOSE classification, its also
classification of THE END RESULTS Used to predict the onset of
degenerative joint disease following LCPD
I – Shape is normal II – loss of head height
< 2 mm deviation of concentric circles Group I & II – “Spherical Congruency”
III – Elliptical head> 2 mm deviation
Contour matches (“Incongrous/Aspherical congruency”)
IV – Flattened head, >1 cm of flattening
Contour matches (“Incongrous/Aspherical congruency”)
Resemblence with Cow’s hip
V – Collapsed head,Contour mismatch (“Incongrous/Aspherical
Incongruency”)
AIMS: Prevention of femoral head deformity
Prevention of secondary degenerative osteoarthritis.
Psychological & Physical development.
Elimination of hip irritability.
Containment of the head.
Restoration good ROM
Prevention subluxation.
Attainment of spherical head at end of disease
For < 2 to 3 yrs – Observation
For >3 yrs –
Parents counseling
Intermittent symptomatic treatment Home traction & physical therapy Hospitalization – loss of ROM Bed Rest Skin Traction – slings & springs NSAIDs
Petrie cast “Broomstick cast”
Snyder sling
TORONTO BRACE
TACHDJIAN BRACE
NEWINGTON BRACE
BIRMINGHAM BRACE
Indication:
Age of clinical onset > 8yrs of age
Herring type B
Radiological evidence of loss of containment by conservative modes
CONTRAINDICATIONS: Herring’s type A and C
Herring’s type B if child less than 8 yrs
Healed cases.
Hinged abduction
ADVANTAGES Ability to obtain permanant
containment of head.
Period of Restriction is only 2 months.
Innominate Osteotomy Varus Derotational Osteotomy
Lateral Shelf procedure
Arthrodiastasis
Advantages: Anterolateral coverage Lengthening of shortened limb No second operation
Disadvantages: Improper coverage in older child Limb length inequality AVN due to raised pressure in joint
Indications:
Failed conservative for containment
8 – 10 yrs
Uncovered head on MRI / Arthrogram
Excessive femoral anteversion
Adv: Maximal coverage in old Excessive femoral anteversion
Disadv: Excessive varus angulation Shortening Gluteal lurch Non / delayed union
2nd sx reqd. for implant removalTrochanteric overgrowth
INDICATION:
Lateral subluxation
Insufficient coverage
Hinged abduction
COMPLICATION: Loss of hip
flexion
lateral femoral cutaneous nerve
Rationale: Widening Unloads the joint
space Reduces pressure
over head Articular cartilage
repair Maintain congruency Allows 50 degree
flexion
Indications & Choice of surgery:
1. Hinged abduction – Valgus subtrochanteric osteotomy
2. Malformed head in catterall gr 3 – Garceau cheilectomy
3. Coxa magna – shelf augmentation
4. Large malformed head with subluxation – VDRO + Pelvic osteotomy
5. Capital physeal arrest & troch overgrowth – Trochanteric advancement or arrest
Failure of lateral end of epiphysis to slide under the edge of acetabulum on an internally rotated & abducted AP X rays is s/o HINGED ABDUCTION.
Combination of VALGUS FLEXION INTERNAL ROTATION
OSTEOTOMY Coxa vara & hinged abduction - valgus Changes articular relations – valgus & flexion External rotation of limb – internal rotation Improve anterolateral head coverage
Indication: Large mushroom head
(coxa plana) Lateral protruberance
Disadv: Physeal slippage Postop joint stiffness
Indications:
Older children with painful hip
Significant femoral head flattenning.
Elevation of GT Shortening of
neck Vertical pull of
muscles Impingement of
GT on rim of aceta – “GEAR STICK SIGN”
Trochanteric Advancement
GT epiphysiodesis
Trapezoidal osteotomy of GT
Lateral calcification
Extent of uncovering of head
Lateral head displacement
Widening of head & neck during early stages (mushroom head)
Saturn phenomenon (sclerotic epiphysis surrounded by ring of lucency)
Premature physeal closure
Shape of Femoral head & congruency with acetabulum – most imp predictor
Age of onset of disease & duration