Case 2M-36,Erythematous rash on

abdomenH/o Alport’s syndrome

Failed renal transplant on hemodialysis

Clinical presentation Alport’s syndrome diagnosed in 1973 –

progressed to ESRF Cadaveric renal transplant in 1992 CAPD commenced in 2005 Peritonitis and subacute bowel obstruction

necessitated a 2nd Cadaveric renal transplant in 2010 PD port removed in 2011

Presenting Symptoms

Generalised abdominal pain Weight loss 20x15cm erythema in periumbilical area All other investigations negative No response to I/V antibiotics Biopsy performed

REACTIVE ANGIOENDOTHELIOMATOSIS

RAE

Clinically- Erythematous violaceous papules Macules, nodules Cellulitis like areas Seen in abdominal areas, thighs and legs Also seen in other sites

RAE

Represents a hypersensitivity reaction Different stimuli- cryoproteins and

microorganisms Vessel occlusion—hypoxaemia—

endothelial proliferation Reported in association with bacterial

endocarditis and other renal diseases.