ans disorders, rsd, hypertonicity
TRANSCRIPT
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MES 2 : ANS Disorders,MES 2 : ANS Disorders,
Reflex Sympathetic Dystrophy,Reflex Sympathetic Dystrophy,
HypertonicityHypertonicity
Ramon Antonio S. Sarmiento ,MDRamon Antonio S. Sarmiento ,MD
DLSU-HSCDLSU-HSC
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ANS DisordersANS Disorders
I.I. Autonomic DysreflexiaAutonomic Dysreflexia
II.II. Central PainCentral Pain
A. CRPSA. CRPSB. Reflex Symat!etic Dystro!yB. Reflex Symat!etic Dystro!y
C. Su"ec#$s atro!yC. Su"ec#$s atro!y
IIIIII. Hyertonicity. Hyertonicity
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Autonomic DysreflexiaAutonomic Dysreflexia
syn"rome of massi%esyn"rome of massi%e
symat!etic "isc!ar&esymat!etic "isc!ar&e
tri&&ere" 'y a noxious stimulitri&&ere" 'y a noxious stimulicommon in SCI atients (it!common in SCI atients (it!
lesions a'o%e )* le%ellesions a'o%e )* le%el
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Clinical ManifestationsClinical Manifestations
+. Hyertension+. Hyertension
. Hea"ac!e. Hea"ac!e
. S(eatin&. S(eatin&. /asal con&estion. /asal con&estion
0. 1acial flus!in&0. 1acial flus!in&
*. Piloerection*. Piloerection2. Reflex 'ra"ycar"ia2. Reflex 'ra"ycar"ia
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Causes Noxious stimuliCauses Noxious stimuli
Bla""er an" 'o(el "istention "ue toBla""er an" 'o(el "istention "ue toneuro&enic 'la""erneuro&enic 'la""er
Pressure soresPressure soresIn&ro(n toenailsIn&ro(n toenails)i&!t clot!in& an" s!oes)i&!t clot!in& an" s!oesUrinary tract infectionsUrinary tract infectionsUterine contractionsUterine contractionsIn%asi%e roce"ureIn%asi%e roce"ure
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!athophysiolo"y!athophysiolo"y
Interrution of in!i'itory si&nalsInterrution of in!i'itory si&nalsPeri!eral an" slanc!nic %asoconstrictiPeri!eral an" slanc!nic %asoconstricti
HyertensionHyertension
Mass symat!etic "isc!ar&es 3Mass symat!etic "isc!ar&es 3
# s(eatin& an" iloerections(eatin& an" iloerection
# Reflex 'ra"ycar"ia an"Reflex 'ra"ycar"ia an"
%aso"ilation 4facial flus!in& an"%aso"ilation 4facial flus!in& an"
con&estion5con&estion5
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!athophysiolo"y!athophysiolo"y
/oxious stimuli/oxious stimuli
ImulsesImulses
Dorsal column 6 Sinot!alamic tractsDorsal column 6 Sinot!alamic tracts In!i'ition of imulsesIn!i'ition of imulses
Symat!etic neuronsSymat!etic neurons
Symat!etic resonseSymat!etic resonse
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ComplicationsComplications
ConfusionConfusion7isual "istur'ance7isual "istur'anceLoss of consciousnessLoss of consciousness8nce!aloat!y8nce!aloat!yIntracere'ral !emorr!a&eIntracere'ral !emorr!a&eSei9uresSei9uresAcute myocar"ial failureAcute myocar"ial failurePulmonary e"emaPulmonary e"ema
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$reatment$reatment
+. I"entify an" remo%e t!e noxious+. I"entify an" remo%e t!e noxious
stimulistimuli
. Sit t!e atient u an" monitor 'loo". Sit t!e atient u an" monitor 'loo"
ressureressure
. Me"ications for !yertension3. Me"ications for !yertension3
/itrates, nife"iine, !y"rala9ine/itrates, nife"iine, !y"rala9ine
. Pre%ention of recurrence. Pre%ention of recurrence
0. Patient an" family e"ucation0. Patient an" family e"ucation
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Central !ainCentral !ain
Pain associate" (it! a central ner%ousPain associate" (it! a central ner%ouslesionlesion
8xamles38xamles3
# )!alamic ain syn"rome)!alamic ain syn"rome# Comlex Re&ional Pain Syn"romesComlex Re&ional Pain Syn"romes4CRPS54CRPS5
# Causal&iaCausal&ia# Reflex Symat!etic Dystro!yReflex Symat!etic Dystro!y44RSD5RSD5
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CR!SCR!S
Clinical fin"in&s3Clinical fin"in&s3
+. Pain an" sensory a'normalities+. Pain an" sensory a'normalities
. A'normal 'loo" flo( an". A'normal 'loo" flo( an" s(eatin&s(eatin&
. A'normality in motor system. A'normality in motor system. )ro!ic c!an&es. )ro!ic c!an&es
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CR!S $ype ':CR!S $ype ':
Reflex Sympathetic DystrophyReflex Sympathetic DystrophySyn"rome t!at "e%elos after aSyn"rome t!at "e%elos after a
noxious e%entnoxious e%ent
not limite" to a eri!eral ner%enot limite" to a eri!eral ner%e
"istri'ution"istri'ution
symtoms "isroortionate tosymtoms "isroortionate tot!e incitin& e%entt!e incitin& e%ent
Distal < roximalDistal < roximal
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Reflex Sympathetic DystrophyReflex Sympathetic Dystrophy
8tiolo&y3 Un#no(n8tiolo&y3 Un#no(n
=t!er terms3=t!er terms3
+. Su"ec#$s atro!y+. Su"ec#$s atro!y. S!oul"er !an" syn"rome. S!oul"er !an" syn"rome
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Sudec()s atrophySudec()s atrophy
Symat!etic symtoms associate"Symat!etic symtoms associate"
(it! traumatic fractures(it! traumatic fractures
Presents (it! ain, L=M, musclePresents (it! ain, L=M, muscleatro!y, cyanosis an" e"emaatro!y, cyanosis an" e"ema
Dia&nostic3 x-rayDia&nostic3 x-ray
In%ol%es "istal extremitiesIn%ol%es "istal extremities
Lasts (ee#s to mont!sLasts (ee#s to mont!s
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Shoulder Hand SyndromeShoulder Hand Syndrome
Associate" (it! coronaryAssociate" (it! coronary
isc!emia an" C7Aisc!emia an" C7A
Painful s!oul"er, !an" an" fin&erPainful s!oul"er, !an" an" fin&erSe%erity not roortional toSe%erity not roortional to
extent of un"erlyin& "isor"erextent of un"erlyin& "isor"er
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RSD: Si"ns and symptomsRSD: Si"ns and symptoms
ain follo(s traumaain follo(s trauma onset3 + mont! after in>uryonset3 + mont! after in>ury
'urnin& an" continuous ain'urnin& an" continuous ain exacer'ate" 'y mo%ement,exacer'ate" 'y mo%ement,
stimulation an" stressstimulation an" stress
4?5 allo"ynia an" !yeral&esia4?5 allo"ynia an" !yeral&esia c!an&e in s#in temerature an"c!an&e in s#in temerature an"
color, e"emacolor, e"ema
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RSD: Si"ns and SymptomsRSD: Si"ns and Symptoms
increase"@ "ecrease" s(eatin&increase"@ "ecrease" s(eatin& imairment of motor functionimairment of motor function
atro!y of s#in an" nailsatro!y of s#in an" nails alterations in !air &ro(t!alterations in !air &ro(t!
loss of >oint mo'ilityloss of >oint mo'ility
(ea#ness an" tremor(ea#ness an" tremor
fluctuatin& si&ns an" symtomsfluctuatin& si&ns an" symtoms
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* Sta"es of RSD* Sta"es of RSD
I. Acute sta&eI. Acute sta&e
# Constant 'urnin& ainConstant 'urnin& ain
# !yeral&esia, !yerest!esia!yeral&esia, !yerest!esia
# !yerat!ia!yerat!ia
# locali9e" e"emalocali9e" e"ema
#increase" !air an" nail &ro(t!increase" !air an" nail &ro(t!
# Increase s#in temeratureIncrease s#in temerature
# muscle (ea#ness, sasmsmuscle (ea#ness, sasms
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Sta"es of RSDSta"es of RSD
II. Dystro!ic sta&eII. Dystro!ic sta&e# !yersensiti%ity an"!yersensiti%ity an"
'urnin& ain'urnin& ain
# lo(ere" s#in temeraturelo(ere" s#in temerature# cessation of !air@ nail &ro(t!cessation of !air@ nail &ro(t!# !yer!y"rosis!yer!y"rosis
# cyanotic s#in colorcyanotic s#in color# muscle atro!ymuscle atro!y# sotty osteoorosissotty osteoorosis
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Sta"es of RSDSta"es of RSD
III. Atro!ic sta&eIII. Atro!ic sta&e
# "ecrease !yersensiti%ity"ecrease !yersensiti%ity
# normali9ation of 'loo" flo(normali9ation of 'loo" flo(an" temeraturean" temerature
# smoot!, &lossy s#insmoot!, &lossy s#in
# se%ere muscle atro!yse%ere muscle atro!y
# "iffuse osteoorosis"iffuse osteoorosis
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RSD: Dia"nosisRSD: Dia"nosis
Difficult to "ia&noseDifficult to "ia&nose
Use anatomic@ !armacolo&icUse anatomic@ !armacolo&ic
ner%e 'loc#sner%e 'loc#s)ec!netium "i!os!onate 'one)ec!netium "i!os!onate 'one
scansscans
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RSD: ComplicationsRSD: Complications
P!le'itisP!le'itis
Inaroriate "ru& useInaroriate "ru& use
Suici"eSuici"e
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RSD: $reatmentRSD: $reatment
)!eraeutic exercise)!eraeutic exerciseSymat!etic ner%e 'loc#sSymat!etic ner%e 'loc#sPsyc!olo&ical counselin&Psyc!olo&ical counselin&P!armacolo&ical inter%ention3P!armacolo&ical inter%ention3
anal&esics, /SAIDS, narcoticsanal&esics, /SAIDS, narcotics
Sur&ery3 r!i9otomies,Sur&ery3 r!i9otomies,cor"otomies, symat!ectomycor"otomies, symat!ectomy
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RSD: $reatmentRSD: $reatment
P!ysical mo"alitiesP!ysical mo"alities- cryot!eray %s. !eat t!eray- cryot!eray %s. !eat t!eray
- )8/S- )8/S
- Acuuncture- AcuunctureBe!a%ioral treatment mo"alitiesBe!a%ioral treatment mo"alities
- Be!a%ior mo"ification@- Be!a%ior mo"ification@
Relaxation tec!ni:ueRelaxation tec!ni:ue- Biofee"'ac#- Biofee"'ac#
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HypertonicityHypertonicity
Increase in muscle toneIncrease in muscle tone
Muscle tone - t!e resistance ofMuscle tone - t!e resistance of
muscle to assi%e elon&ation ormuscle to assi%e elon&ation or
stretc!stretc!A'normalities3A'normalities3
+. Hyertonia+. Hyertonia
. Hyotonia. Hyotonia
. Dystonia. Dystonia
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Muscle $one DisordersMuscle $one Disorders
SasticitySasticity
Ri&i"ityRi&i"ity
Hyotonia@ 1lacci"ityHyotonia@ 1lacci"ity
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SpasticitySpasticity
7elocity-"een"ent increase intonic stretc! reflexes (it!exa&&erate" !asic stretc!reflexes
Results from "ysfunctional sinalan" surasinal mec!anisms
A comonent of uer motorneuron syn"rome
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Conditions presentin"Conditions presentin"
+ith Spasticity+ith Spasticity+.+. Sinal cor" in>urySinal cor" in>ury
.. Demyelinatin& "iseaseDemyelinatin& "isease
.. Stro#eStro#e
.. )raumatic 'rain in>ury)raumatic 'rain in>ury
0.0. Decorticate an" "ecere'rateDecorticate an" "ecere'rateri&i"ityri&i"ity
*.*. Cere'ral alsyCere'ral alsy
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Spasticity: symptomsSpasticity: symptoms
a'normal reflex 'e!a%iora'normal reflex 'e!a%ior
loss of autonomic controlloss of autonomic control
imaire" muscle acti%ationimaire" muscle acti%ationaresisaresis
"ecrease" "exterity"ecrease" "exterity
fati&a'ilityfati&a'ility
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Spasticity: Clinical EaluationSpasticity: Clinical Ealuation
Clinical !istoryClinical !istory
Reflex examinationReflex examination
Passi%e an" acti%e motionPassi%e an" acti%e motionexaminationexamination
1unctional examination1unctional examination
Determine (!et!er sasticity isDetermine (!et!er sasticity is
'eneficial or "etrimental'eneficial or "etrimental
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-enefits from spasticity-enefits from spasticity
Ai" to stan"in& an" (al#in&Ai" to stan"in& an" (al#in&
Maintaine" muscle massMaintaine" muscle mass
Maintaine" 'one minerali9ationMaintaine" 'one minerali9ationRe"uce" "een"ent e"emaRe"uce" "een"ent e"ema
Re"uce" ris# of "ee %enousRe"uce" ris# of "ee %enous
t!rom'osist!rom'osis
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Detrimental effects of spasticityDetrimental effects of spasticity
Imaire" stan"in& 'alanceImaire" stan"in& 'alance
Imaire" s(in& !ase of &aitImaire" s(in& !ase of &ait
Slo( %oluntary mo%ementsSlo( %oluntary mo%ementsRis# of contractureRis# of contracture
Imaire" slee, erineal !y&ieneImaire" slee, erineal !y&iene
PainPain
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Spasticity: $reatmentSpasticity: $reatment
8liminate nocicetion8liminate nocicetion
Pro%i"e atient e"ucation an"Pro%i"e atient e"ucation an"
a"ati%e e:uimenta"ati%e e:uimentRan&e of motion exercisesRan&e of motion exercises
Proer seatin& an" ositionin&Proer seatin& an" ositionin&
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Spasticity: $reatmentSpasticity: $reatment
Daily R=M an" static stretc!Daily R=M an" static stretc!
Bracin&, slintin&Bracin&, slintin&
Biofee"'ac#, 8SBiofee"'ac#, 8SIcin&Icin&
Sur&ery3 )en"on len&t!enin&,Sur&ery3 )en"on len&t!enin&,
selecti%e "orsal r!i9otomy,selecti%e "orsal r!i9otomy,
tenotomytenotomy
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Spasticity: $reatmentSpasticity: $reatment
=ral3 Baclofen, Cloni"ine,=ral3 Baclofen, Cloni"ine,
Dia9eam, )i9ani"ine,Dia9eam, )i9ani"ine,
DantroleneDantroleneIntrat!ecal BaclofenIntrat!ecal Baclofen
C!emical ner%e 'loc#s3 B=)=C!emical ner%e 'loc#s3 B=)=
in>ection, P!enol 'loc#in>ection, P!enol 'loc#
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Ri"idityRi"idity
Resistance is increase" in 'ot!Resistance is increase" in 'ot!a&onist an" anta&onist musclesa&onist an" anta&onist muscles
Bo"y arts 'ecome stiff an"Bo"y arts 'ecome stiff an"immo%a'leimmo%a'leSeen in lesions of 'asal &an&liaSeen in lesions of 'asal &an&lia
e.&. Par#inson$s "iseasee.&. Par#inson$s "iseaseDue to excessi%e surasinalDue to excessi%e surasinalmec!anismmec!anism
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Ri"idityRi"idity
Associate" (it!3Associate" (it!3
# 'ra"y#inesia'ra"y#inesia
# tremortremor# loss of ostural sta'ilityloss of ostural sta'ility
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$ypes of Ri"idity$ypes of Ri"idity
Cogwheel rigidityCogwheel rigidity - rac!etli#e- rac!etli#e
resonse to assi%e mo%ement resonse to assi%e mo%ement
alternatin& lettin& &o an"alternatin& lettin& &o an"
increasin& resistance toincreasin& resistance to
mo%ementmo%ement
Leadpipe rigidityLeadpipe rigidity ; ri&i"ity; ri&i"ityconstant t!rou&!out t!econstant t!rou&!out t!e
mo%ementmo%ement
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Hypotonia and .laccidityHypotonia and .laccidity
Decrease" or a'sent muscularDecrease" or a'sent muscular
tonetone
Diminis!e" resistance to assi%eDiminis!e" resistance to assi%emo%ementmo%ement
Imaire" mo%ementsImaire" mo%ements
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Hypotonia and .laccidityHypotonia and .laccidity
Seen in t!e follo(in& con"itions3Seen in t!e follo(in& con"itions3
+. UM/ lesions affectin&+. UM/ lesions affectin&
cere'ellum or yrami"al tracts cere'ellum or yrami"al tracts. Sinal or cere'ral s!oc#. Sinal or cere'ral s!oc#
. LM/ lesions affectin& P/S. LM/ lesions affectin& P/S