ans disorders, rsd, hypertonicity

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    MES 2 : ANS Disorders,MES 2 : ANS Disorders,

    Reflex Sympathetic Dystrophy,Reflex Sympathetic Dystrophy,

    HypertonicityHypertonicity

    Ramon Antonio S. Sarmiento ,MDRamon Antonio S. Sarmiento ,MD

    DLSU-HSCDLSU-HSC

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    ANS DisordersANS Disorders

    I.I. Autonomic DysreflexiaAutonomic Dysreflexia

    II.II. Central PainCentral Pain

    A. CRPSA. CRPSB. Reflex Symat!etic Dystro!yB. Reflex Symat!etic Dystro!y

    C. Su"ec#$s atro!yC. Su"ec#$s atro!y

    IIIIII. Hyertonicity. Hyertonicity

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    Autonomic DysreflexiaAutonomic Dysreflexia

    syn"rome of massi%esyn"rome of massi%e

    symat!etic "isc!ar&esymat!etic "isc!ar&e

    tri&&ere" 'y a noxious stimulitri&&ere" 'y a noxious stimulicommon in SCI atients (it!common in SCI atients (it!

    lesions a'o%e )* le%ellesions a'o%e )* le%el

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    Clinical ManifestationsClinical Manifestations

    +. Hyertension+. Hyertension

    . Hea"ac!e. Hea"ac!e

    . S(eatin&. S(eatin&. /asal con&estion. /asal con&estion

    0. 1acial flus!in&0. 1acial flus!in&

    *. Piloerection*. Piloerection2. Reflex 'ra"ycar"ia2. Reflex 'ra"ycar"ia

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    Causes Noxious stimuliCauses Noxious stimuli

    Bla""er an" 'o(el "istention "ue toBla""er an" 'o(el "istention "ue toneuro&enic 'la""erneuro&enic 'la""er

    Pressure soresPressure soresIn&ro(n toenailsIn&ro(n toenails)i&!t clot!in& an" s!oes)i&!t clot!in& an" s!oesUrinary tract infectionsUrinary tract infectionsUterine contractionsUterine contractionsIn%asi%e roce"ureIn%asi%e roce"ure

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    !athophysiolo"y!athophysiolo"y

    Interrution of in!i'itory si&nalsInterrution of in!i'itory si&nalsPeri!eral an" slanc!nic %asoconstrictiPeri!eral an" slanc!nic %asoconstricti

    HyertensionHyertension

    Mass symat!etic "isc!ar&es 3Mass symat!etic "isc!ar&es 3

    # s(eatin& an" iloerections(eatin& an" iloerection

    # Reflex 'ra"ycar"ia an"Reflex 'ra"ycar"ia an"

    %aso"ilation 4facial flus!in& an"%aso"ilation 4facial flus!in& an"

    con&estion5con&estion5

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    !athophysiolo"y!athophysiolo"y

    /oxious stimuli/oxious stimuli

    ImulsesImulses

    Dorsal column 6 Sinot!alamic tractsDorsal column 6 Sinot!alamic tracts In!i'ition of imulsesIn!i'ition of imulses

    Symat!etic neuronsSymat!etic neurons

    Symat!etic resonseSymat!etic resonse

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    ComplicationsComplications

    ConfusionConfusion7isual "istur'ance7isual "istur'anceLoss of consciousnessLoss of consciousness8nce!aloat!y8nce!aloat!yIntracere'ral !emorr!a&eIntracere'ral !emorr!a&eSei9uresSei9uresAcute myocar"ial failureAcute myocar"ial failurePulmonary e"emaPulmonary e"ema

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    $reatment$reatment

    +. I"entify an" remo%e t!e noxious+. I"entify an" remo%e t!e noxious

    stimulistimuli

    . Sit t!e atient u an" monitor 'loo". Sit t!e atient u an" monitor 'loo"

    ressureressure

    . Me"ications for !yertension3. Me"ications for !yertension3

    /itrates, nife"iine, !y"rala9ine/itrates, nife"iine, !y"rala9ine

    . Pre%ention of recurrence. Pre%ention of recurrence

    0. Patient an" family e"ucation0. Patient an" family e"ucation

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    Central !ainCentral !ain

    Pain associate" (it! a central ner%ousPain associate" (it! a central ner%ouslesionlesion

    8xamles38xamles3

    # )!alamic ain syn"rome)!alamic ain syn"rome# Comlex Re&ional Pain Syn"romesComlex Re&ional Pain Syn"romes4CRPS54CRPS5

    # Causal&iaCausal&ia# Reflex Symat!etic Dystro!yReflex Symat!etic Dystro!y44RSD5RSD5

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    CR!SCR!S

    Clinical fin"in&s3Clinical fin"in&s3

    +. Pain an" sensory a'normalities+. Pain an" sensory a'normalities

    . A'normal 'loo" flo( an". A'normal 'loo" flo( an" s(eatin&s(eatin&

    . A'normality in motor system. A'normality in motor system. )ro!ic c!an&es. )ro!ic c!an&es

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    CR!S $ype ':CR!S $ype ':

    Reflex Sympathetic DystrophyReflex Sympathetic DystrophySyn"rome t!at "e%elos after aSyn"rome t!at "e%elos after a

    noxious e%entnoxious e%ent

    not limite" to a eri!eral ner%enot limite" to a eri!eral ner%e

    "istri'ution"istri'ution

    symtoms "isroortionate tosymtoms "isroortionate tot!e incitin& e%entt!e incitin& e%ent

    Distal < roximalDistal < roximal

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    Reflex Sympathetic DystrophyReflex Sympathetic Dystrophy

    8tiolo&y3 Un#no(n8tiolo&y3 Un#no(n

    =t!er terms3=t!er terms3

    +. Su"ec#$s atro!y+. Su"ec#$s atro!y. S!oul"er !an" syn"rome. S!oul"er !an" syn"rome

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    Sudec()s atrophySudec()s atrophy

    Symat!etic symtoms associate"Symat!etic symtoms associate"

    (it! traumatic fractures(it! traumatic fractures

    Presents (it! ain, L=M, musclePresents (it! ain, L=M, muscleatro!y, cyanosis an" e"emaatro!y, cyanosis an" e"ema

    Dia&nostic3 x-rayDia&nostic3 x-ray

    In%ol%es "istal extremitiesIn%ol%es "istal extremities

    Lasts (ee#s to mont!sLasts (ee#s to mont!s

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    Shoulder Hand SyndromeShoulder Hand Syndrome

    Associate" (it! coronaryAssociate" (it! coronary

    isc!emia an" C7Aisc!emia an" C7A

    Painful s!oul"er, !an" an" fin&erPainful s!oul"er, !an" an" fin&erSe%erity not roortional toSe%erity not roortional to

    extent of un"erlyin& "isor"erextent of un"erlyin& "isor"er

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    RSD: Si"ns and symptomsRSD: Si"ns and symptoms

    ain follo(s traumaain follo(s trauma onset3 + mont! after in>uryonset3 + mont! after in>ury

    'urnin& an" continuous ain'urnin& an" continuous ain exacer'ate" 'y mo%ement,exacer'ate" 'y mo%ement,

    stimulation an" stressstimulation an" stress

    4?5 allo"ynia an" !yeral&esia4?5 allo"ynia an" !yeral&esia c!an&e in s#in temerature an"c!an&e in s#in temerature an"

    color, e"emacolor, e"ema

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    RSD: Si"ns and SymptomsRSD: Si"ns and Symptoms

    increase"@ "ecrease" s(eatin&increase"@ "ecrease" s(eatin& imairment of motor functionimairment of motor function

    atro!y of s#in an" nailsatro!y of s#in an" nails alterations in !air &ro(t!alterations in !air &ro(t!

    loss of >oint mo'ilityloss of >oint mo'ility

    (ea#ness an" tremor(ea#ness an" tremor

    fluctuatin& si&ns an" symtomsfluctuatin& si&ns an" symtoms

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    * Sta"es of RSD* Sta"es of RSD

    I. Acute sta&eI. Acute sta&e

    # Constant 'urnin& ainConstant 'urnin& ain

    # !yeral&esia, !yerest!esia!yeral&esia, !yerest!esia

    # !yerat!ia!yerat!ia

    # locali9e" e"emalocali9e" e"ema

    #increase" !air an" nail &ro(t!increase" !air an" nail &ro(t!

    # Increase s#in temeratureIncrease s#in temerature

    # muscle (ea#ness, sasmsmuscle (ea#ness, sasms

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    Sta"es of RSDSta"es of RSD

    II. Dystro!ic sta&eII. Dystro!ic sta&e# !yersensiti%ity an"!yersensiti%ity an"

    'urnin& ain'urnin& ain

    # lo(ere" s#in temeraturelo(ere" s#in temerature# cessation of !air@ nail &ro(t!cessation of !air@ nail &ro(t!# !yer!y"rosis!yer!y"rosis

    # cyanotic s#in colorcyanotic s#in color# muscle atro!ymuscle atro!y# sotty osteoorosissotty osteoorosis

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    Sta"es of RSDSta"es of RSD

    III. Atro!ic sta&eIII. Atro!ic sta&e

    # "ecrease !yersensiti%ity"ecrease !yersensiti%ity

    # normali9ation of 'loo" flo(normali9ation of 'loo" flo(an" temeraturean" temerature

    # smoot!, &lossy s#insmoot!, &lossy s#in

    # se%ere muscle atro!yse%ere muscle atro!y

    # "iffuse osteoorosis"iffuse osteoorosis

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    RSD: Dia"nosisRSD: Dia"nosis

    Difficult to "ia&noseDifficult to "ia&nose

    Use anatomic@ !armacolo&icUse anatomic@ !armacolo&ic

    ner%e 'loc#sner%e 'loc#s)ec!netium "i!os!onate 'one)ec!netium "i!os!onate 'one

    scansscans

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    RSD: ComplicationsRSD: Complications

    P!le'itisP!le'itis

    Inaroriate "ru& useInaroriate "ru& use

    Suici"eSuici"e

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    RSD: $reatmentRSD: $reatment

    )!eraeutic exercise)!eraeutic exerciseSymat!etic ner%e 'loc#sSymat!etic ner%e 'loc#sPsyc!olo&ical counselin&Psyc!olo&ical counselin&P!armacolo&ical inter%ention3P!armacolo&ical inter%ention3

    anal&esics, /SAIDS, narcoticsanal&esics, /SAIDS, narcotics

    Sur&ery3 r!i9otomies,Sur&ery3 r!i9otomies,cor"otomies, symat!ectomycor"otomies, symat!ectomy

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    RSD: $reatmentRSD: $reatment

    P!ysical mo"alitiesP!ysical mo"alities- cryot!eray %s. !eat t!eray- cryot!eray %s. !eat t!eray

    - )8/S- )8/S

    - Acuuncture- AcuunctureBe!a%ioral treatment mo"alitiesBe!a%ioral treatment mo"alities

    - Be!a%ior mo"ification@- Be!a%ior mo"ification@

    Relaxation tec!ni:ueRelaxation tec!ni:ue- Biofee"'ac#- Biofee"'ac#

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    HypertonicityHypertonicity

    Increase in muscle toneIncrease in muscle tone

    Muscle tone - t!e resistance ofMuscle tone - t!e resistance of

    muscle to assi%e elon&ation ormuscle to assi%e elon&ation or

    stretc!stretc!A'normalities3A'normalities3

    +. Hyertonia+. Hyertonia

    . Hyotonia. Hyotonia

    . Dystonia. Dystonia

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    Muscle $one DisordersMuscle $one Disorders

    SasticitySasticity

    Ri&i"ityRi&i"ity

    Hyotonia@ 1lacci"ityHyotonia@ 1lacci"ity

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    SpasticitySpasticity

    7elocity-"een"ent increase intonic stretc! reflexes (it!exa&&erate" !asic stretc!reflexes

    Results from "ysfunctional sinalan" surasinal mec!anisms

    A comonent of uer motorneuron syn"rome

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    Conditions presentin"Conditions presentin"

    +ith Spasticity+ith Spasticity+.+. Sinal cor" in>urySinal cor" in>ury

    .. Demyelinatin& "iseaseDemyelinatin& "isease

    .. Stro#eStro#e

    .. )raumatic 'rain in>ury)raumatic 'rain in>ury

    0.0. Decorticate an" "ecere'rateDecorticate an" "ecere'rateri&i"ityri&i"ity

    *.*. Cere'ral alsyCere'ral alsy

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    Spasticity: symptomsSpasticity: symptoms

    a'normal reflex 'e!a%iora'normal reflex 'e!a%ior

    loss of autonomic controlloss of autonomic control

    imaire" muscle acti%ationimaire" muscle acti%ationaresisaresis

    "ecrease" "exterity"ecrease" "exterity

    fati&a'ilityfati&a'ility

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    Spasticity: Clinical EaluationSpasticity: Clinical Ealuation

    Clinical !istoryClinical !istory

    Reflex examinationReflex examination

    Passi%e an" acti%e motionPassi%e an" acti%e motionexaminationexamination

    1unctional examination1unctional examination

    Determine (!et!er sasticity isDetermine (!et!er sasticity is

    'eneficial or "etrimental'eneficial or "etrimental

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    -enefits from spasticity-enefits from spasticity

    Ai" to stan"in& an" (al#in&Ai" to stan"in& an" (al#in&

    Maintaine" muscle massMaintaine" muscle mass

    Maintaine" 'one minerali9ationMaintaine" 'one minerali9ationRe"uce" "een"ent e"emaRe"uce" "een"ent e"ema

    Re"uce" ris# of "ee %enousRe"uce" ris# of "ee %enous

    t!rom'osist!rom'osis

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    Detrimental effects of spasticityDetrimental effects of spasticity

    Imaire" stan"in& 'alanceImaire" stan"in& 'alance

    Imaire" s(in& !ase of &aitImaire" s(in& !ase of &ait

    Slo( %oluntary mo%ementsSlo( %oluntary mo%ementsRis# of contractureRis# of contracture

    Imaire" slee, erineal !y&ieneImaire" slee, erineal !y&iene

    PainPain

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    Spasticity: $reatmentSpasticity: $reatment

    8liminate nocicetion8liminate nocicetion

    Pro%i"e atient e"ucation an"Pro%i"e atient e"ucation an"

    a"ati%e e:uimenta"ati%e e:uimentRan&e of motion exercisesRan&e of motion exercises

    Proer seatin& an" ositionin&Proer seatin& an" ositionin&

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    Spasticity: $reatmentSpasticity: $reatment

    Daily R=M an" static stretc!Daily R=M an" static stretc!

    Bracin&, slintin&Bracin&, slintin&

    Biofee"'ac#, 8SBiofee"'ac#, 8SIcin&Icin&

    Sur&ery3 )en"on len&t!enin&,Sur&ery3 )en"on len&t!enin&,

    selecti%e "orsal r!i9otomy,selecti%e "orsal r!i9otomy,

    tenotomytenotomy

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    Spasticity: $reatmentSpasticity: $reatment

    =ral3 Baclofen, Cloni"ine,=ral3 Baclofen, Cloni"ine,

    Dia9eam, )i9ani"ine,Dia9eam, )i9ani"ine,

    DantroleneDantroleneIntrat!ecal BaclofenIntrat!ecal Baclofen

    C!emical ner%e 'loc#s3 B=)=C!emical ner%e 'loc#s3 B=)=

    in>ection, P!enol 'loc#in>ection, P!enol 'loc#

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    Ri"idityRi"idity

    Resistance is increase" in 'ot!Resistance is increase" in 'ot!a&onist an" anta&onist musclesa&onist an" anta&onist muscles

    Bo"y arts 'ecome stiff an"Bo"y arts 'ecome stiff an"immo%a'leimmo%a'leSeen in lesions of 'asal &an&liaSeen in lesions of 'asal &an&lia

    e.&. Par#inson$s "iseasee.&. Par#inson$s "iseaseDue to excessi%e surasinalDue to excessi%e surasinalmec!anismmec!anism

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    Ri"idityRi"idity

    Associate" (it!3Associate" (it!3

    # 'ra"y#inesia'ra"y#inesia

    # tremortremor# loss of ostural sta'ilityloss of ostural sta'ility

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    $ypes of Ri"idity$ypes of Ri"idity

    Cogwheel rigidityCogwheel rigidity - rac!etli#e- rac!etli#e

    resonse to assi%e mo%ement resonse to assi%e mo%ement

    alternatin& lettin& &o an"alternatin& lettin& &o an"

    increasin& resistance toincreasin& resistance to

    mo%ementmo%ement

    Leadpipe rigidityLeadpipe rigidity ; ri&i"ity; ri&i"ityconstant t!rou&!out t!econstant t!rou&!out t!e

    mo%ementmo%ement

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    Hypotonia and .laccidityHypotonia and .laccidity

    Decrease" or a'sent muscularDecrease" or a'sent muscular

    tonetone

    Diminis!e" resistance to assi%eDiminis!e" resistance to assi%emo%ementmo%ement

    Imaire" mo%ementsImaire" mo%ements

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    Hypotonia and .laccidityHypotonia and .laccidity

    Seen in t!e follo(in& con"itions3Seen in t!e follo(in& con"itions3

    +. UM/ lesions affectin&+. UM/ lesions affectin&

    cere'ellum or yrami"al tracts cere'ellum or yrami"al tracts. Sinal or cere'ral s!oc#. Sinal or cere'ral s!oc#

    . LM/ lesions affectin& P/S. LM/ lesions affectin& P/S