{ carpal fusion jalal jalal shokouhi-md, isr kimia kahrizi-md, prof. of medical genetics mohammad...
TRANSCRIPT
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{
Carpal fusion
Jalal Jalal Shokouhi-MD, ISRKimia Kahrizi-MD, Prof. of medical geneticsMohammad hossein Herischi-MD,PhD-Baku, Republic AzerbaijanShahyar Pashaei-PhD, Boniad daneshname negari, IranAliakbar Ameri-MD, Jaam e jam
j a l a l j a l a l s h o k o uh i@ho tma i l . c om
www.medimage. i r
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1. Hereditary2. Non-hereditary
Causes:
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Carpal fusion is hereditary and nonhereditary conditions in acrocallosal syndrome, acromegaly, apert, arthrograyposis, carpenter syndrome, chromosal abnormalities, EEC syndrome, F syndrome, fetal alcohol syndrome, holt oram S. leopard S., multiple synostosis S., oligosyndactyly S., Pfeiffer-likes, scleroderma, split hand and foot, stickler S., thalidomide embryopathy, turner syndrome and many other conditions (taybi syndrome book).Sometimes there is no known causative disease
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Technic = X-ray
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Hand bone anomalies are more common in syndromes or other congenital or non-hereditary conditions but polydactyly, syndactyly or oligodactyly and carpal fusions are interesting.X-ray is the modality of choice but MRI and X-ray CT with multiplanar reconstructions can be use for diagnosis.
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Short second phalanx of fifth finger
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Short second phalanx of fifth fingerRight hand with three metacarpal and phalanx, fused carpal bones
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Fused right carpal bones capitate and hamate
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Gallery
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